Superior semicircular canal dehiscence syndrome: a new aetiology

Puwanarajah, P; Pretorius, Pieter; Bottrill, Ian

doi:10.1017/s0022215108001965

Cited by 18 publications

(8 citation statements)

References 9 publications

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“…This CT scan also shows a groove from the superior petrosal sinus on the temporal bone adjacent to the dehiscence. A recent case report has suggested that such developmental abnormalities may account for some cases of the Tullio phenomenon [33].…”

Section: Ocular Movementsmentioning

confidence: 99%

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The Tullio phenomenon: a neurologically neglected presentation

et al. 2011

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The Tullio phenomenon refers to sound-induced disequilibrium or oscillopsia. Patients with this condition frequently present to neurologists, many of whom are unfamiliar with the condition and its diagnostic criteria. Indeed, due to the unusual nature of the symptoms patients are often misdiagnosed as having psychiatric disturbances. Tullio patients describe disequilibrium, auditory and visual symptoms, which are recurrent, brief, and often triggered by loud noises or middle ear pressure changes, e.g. the Valsalva manoeuvre. Many cases are associated with superior semicircular canal dehiscence (SCCD). Early work suggested that the presence of sound-induced torsional eye movements and visual field tilts were consequent upon a utricular-mediated ocular tilt reaction. However, more recent evidence from imaging and oculographic research, as well as data from our patient series indicates that these ocular abnormalities are usually the result of superior semicircular canal stimulation. The clinical history and a focussed examination are often sufficient to make the diagnosis, which can be confirmed with high resolution CT imaging of the temporal bones. In some patients, surgical occlusion or resurfacing of the affected canal can ameliorate symptoms and signs. The aim of this paper is two-fold: Firstly, to review the clinical features of the Tullio phenomenon, and secondly, to highlight our own observations in three cases with a new clinical syndrome consisting of Tullio's phenomenon with bilateral vestibular failure, a pure horizontal nystagmus in response to sound, and no evidence of canal dehiscence.

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Section: Ocular Movementsmentioning

confidence: 99%

“…Although this may be regarded a normal anatomical variant, it has been suggested that such developmental abnormalities may underlie some cases of Tullio phenomenon (see Ref. [33])…”

Section: Ocular Movementsmentioning

confidence: 99%

The Tullio phenomenon: a neurologically neglected presentation

et al. 2011

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“…When the SCC is too close to the developing dura, cartilage formation covering the superior part of the SSC may be disturbed, leading to a bone defect on the roof of the SSC. An enlarged superior petrosal sinus was also reported to be a cause of SCD and this was also explained in the same manner [17].…”

Section: Discussionmentioning

confidence: 78%

Anatomical feature of the middle cranial fossa in fetal periods: Possible etiology of superior canal dehiscence syndrome

Takahashi

Tsunoda

Shirakura

et al. 2011

Acta Oto-Laryngologica

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“…Involvement of the petrosal sinus with SCD has been documented in a number of case reports [25,26] and several case series [2,13,19]. They report SPS involvement in 9-32%.…”

Section: Discussionmentioning

confidence: 99%