Superior vena cava syndrome after correction of partial anomalous pulmonary venous connection

Abstract

Partial anomalous pulmonary venous connection (PAPVС) is an infrequent congenital heart defect. We report a case of rare complication following the correction of PAPVС in a 55 years-old male. On the fourth postoperative day after surgical correction of the mentioned congenital defect, our patient suddenly developed the superior vena cava (SVC) syndrome. Computed tomography revealed thrombosis of the upper part of the SVC. Following ineffective thrombolytic therapy, an urgent re-do surgery was performed. Iatrogenic narrowing of the SVC was found at its ostia to the right atrium. The SVC was fully occluded by thrombus up to the inflow of the innominate vein. The patient underwent successful thrombectomy and patch repair of the SVC.