Surgical repair of Ebstein's malformation associated with atrioventricular septal defect (atrioventricular canal)

Knott‐Craig, Christopher J.; Merwe, P L Van der; Kalis, Neale Nicola; Hunter, James A.

doi:10.1016/s0022-5223(19)34658-6

Cited by 6 publications

(3 citation statements)

References 6 publications

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“…We performed a literature review and found 22 documented cases of Ebstein's anomaly with an AVCD [2][3][4]. The ages of the surgically managed patients ranged from 0.25 to 20 years.…”

Section: Discussionmentioning

confidence: 99%

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Antenatal Diagnosis of a Partial Atrioventricular Canal with Ebstein’s Anomaly

et al. 2021

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The simultaneous occurrence of an atrioventricular canal defect (AVCD) and Ebstein’s anomaly is extremely rare, occurring in less than 0.5% of all patients with AVCD. Only 22 cases are described in the literature. This patient’s antenatal diagnosis of both Ebstein’s anomaly and partial AVCD was made at 25 weeks of gestation. The delivery was organized in a tertiary center. The initial neonatal course was difficult but with adequate treatment, a rapid improvement allowed for a gap of almost 2 years before a complete surgical repair including a cone tricuspid plasty. To our knowledge, this is the first case of antenatal diagnosis, with carefully tailored delivery, neonatal care and subsequent follow-up before indication for successful surgery.

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“…We performed a literature review and found 22 documented cases of Ebstein's anomaly with an AVCD [2][3][4]. The ages of the surgically managed patients ranged from 0.25 to 20 years.…”

Section: Discussionmentioning

confidence: 99%

“…We performed a literature review and found 22 cases, including 16 partial, 3 intermediate and 3 complete AVCD cases. In most cases, the diagnosis was made postmortem via necropsy or during surgery [1,3,4]. The ages of the surgically managed patients ranged from 0.25 to 20 years.…”

Section: Introductionmentioning

confidence: 99%

Antenatal Diagnosis of a Partial Atrioventricular Canal with Ebstein’s Anomaly

et al. 2021

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“…Knott-Craig et al published a report with 12 previously described cases. 4 There have been infrequent case reports of surgical correction of the anomaly. The majority of such cases mentioned in the literature have been diagnosed at autopsy.…”

Section: Discussionmentioning

confidence: 99%

Secondary Repair of Ebstein's Anomaly With Atrioventricular Septal Defect Using the Cone Technique

Gaurav

Panda

Gooi

et al. 2013

World J Pediatr Congenit Heart Surg

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A nine-year-old boy with incomplete atrioventricular septal defect (AVSD) and Ebstein's anomaly had undergone a closure of primum atrial septal defect and repair of right and left AV valves at four years of age. He presented with severe regurgitation of the right AV valve. He underwent further surgery, and a cone reconstruction of the right AV valve was performed. The association of Ebstein's anomaly with AVSD has been reported only rarely. We present a case of this association treated with the previously unreported application of the cone reconstruction (da Silva repair) as a secondary strategy.

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