Surgical strategy for congenital blepharophimosis syndrome

Huang, Weiqing; Qiao, Qun; Zhao, Ru; Wang, Xiaojun; Fang, Xue-quan

doi:10.1097/00029330-200708020-00007

Cited by 11 publications

(3 citation statements)

References 20 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…But most surgeons who advocated one-stage surgical treatment had addressed single-stage correction of epicanthus inversus along with ptosis only and had ignored the correction order of other two steps which may affect the adjustment of vertical and horizontal lengths of eyelids. [ 5 6 ]…”

mentioning

confidence: 99%

Single stage surgery for Blepharophimosis syndrome

Bhattacharjee

Kuri

et al. 2012

Indian J Ophthalmol

View full text Add to dashboard Cite

Purpose:The purpose of this study was to report the functional and cosmetic outcome of single stage surgical procedure for correction of the classic components of Blepharophimosis syndrome.Materials and Methods:We report a retrospective case file review of 11 patients with Blepharophimosis syndrome operated between July 2004 and April 2008. Each patient had undergone the correction of epicanthus inversus, telecanthus, palpebral phimosis, and bilateral ptosis as a single-stage surgical procedure. Patients were examined and photographed before and after surgery. The mean follow-up was 3 years (range 2-6 years).Results:A total of 11 patients (8 males, 3 females) with a mean age of 9 years (range 6--22 years) were reviewed. The surgical outcome was assessed both functionally and cosmetically. The mean preoperative visual acuity was 0.729 ± 0.316 SD and the mean postoperative visual acuity was 0.856 ± 0.277 SD (P <0.0428). There was a statistically significant decrease of astigmatism following ptosis correction (P<0.05), improvement of telecanthus (P<0.0001) in terms of IICD (inner intercanthal distance), and HPFL (horizontal palpebral fissure length) (P=0.019) along with improvement of the superior visual field. The mean preoperative and postoperative IICD was 3±0.33 SD and 2.418 ± 0.189 SD, respectively. There was also a significant postoperative improvement of ptosis (P< 0.01), as measured by IPFH (vertical interpalpebral fissure height). All the patients had a stable functional and cosmetic result after a mean follow-up period of 3 years.Conclusion:Single-stage surgical correction of the classic anomalies of Blepharophimosis syndrome provides stable and successful long-term results.

show abstract

mentioning

confidence: 99%

Single stage surgery for Blepharophimosis syndrome

Bhattacharjee

Kuri

et al. 2012

Indian J Ophthalmol

View full text Add to dashboard Cite

show abstract

“…Most of the known surgical techniques for BPS include multistage procedures. The surgical treatment includes multiple surgical procedures done between 3- and 9-months interval which needs repeated hospitalization and prolonged follow- up [ 11 , 12 ].…”

Section: Discussionmentioning

confidence: 99%

Surgical outcome of epicanthus and telecanthus correction by C-U medial canthoplasty with lateral canthoplasty in treatment of Blepharophimosis syndrome

et al. 2022

View full text Add to dashboard Cite

Purpose To evaluate the surgical outcome of epicanthus and telecanthus correction by C-U medial canthoplasty with lateral canthoplasty in Blepharophimosis Syndrome. Patients and methods This was a retrospective single arm interventional study including 18 eyes of 9 patients with Blepharophimosis-ptosis-epicanthus inversus syndrome who presented to oculoplastic clinic, ophthalmology department, Qena university hospital in the period of between July 2020 to April 2021. All the patients had BPES with epicanthus and telecanthus. All cases were subjected to by C plasty with medial and lateral canthoplasty for correction of epicanthus and telecanthus correction followed by frontalis suspension surgery to correct the co-existing blepharoptosis. Results The study included 9 cases of BPES, 6 boys and 3 girls, the mean age was 5.4 ± 1.5 in the study group, all patients had a positive family history for BPES. After surgery, the mean IICD decreased from 38.44 mm preoperatively to 32.8 mm postoperatively, with a mean difference of 6.2 mm (P < 0.001). Likewise, the mean PFL increased from 20.78 mm preoperatively to 26.63 mm postoperatively, with a mean difference of 5.8 mm (P < 0.001). Epicanthus skin fold disappeared in all cases and medical canthus could be seen with well healed difficulty seen scars. Conclusion C-U medial canthoplasty with lateral canthoplasty in Blepharophimosis Syndrome was found to be an effective procedure in the correction of epicanthus and telecanthus.

show abstract

“…Two out of 18 (11%) patients with PFHs more than 2 mm needed a repeat operation, but all five (100%) patients with less than 2 mm (very severe ptosis) needed repeat operations. 6 A total of 11 patients (8 males, 3 females) with a mean age of 9 years (range 6--22 years) were reviewed. The surgical outcome was assessed both functionally and cosmetically in single stage surgery.…”

Section: Discussionmentioning

confidence: 99%

Surgical outcome of blepharophimosis syndrome: Double vs single stage

Kadir¹

2019

IJOOO

View full text Add to dashboard Cite

Purpose: To assess the surgical outcome of Blepharophimosis syndrome (BPES). Materials and Methods: This interventional study has been evaluated pre and postoperatively of fifty patients in two tertiary eye hospital in Bangladesh. All patients were divided into two groups like as group-A (35 patients) and group-B (15 patients). Telecanthus, Epicanthus and ptosis were corrected 3 months apart in group-A. All procedures were done in single setting in group-B. Results: Male patients were 21 (42%) and female patients were 29 (58%). In group-A, Satisfactory outcome of Y-V plasty was 89%, and 11% patient presented unsatisfactory correction of telecanthus. Under correction after ptosis surgery was observed in 02 patients. In group-B, satisfactory outcome of C-V plasty was 93% and under correction was observed in 4 patients followed by ptosis surgery. Conclusion: There is no significant difference between Y-V plasty and C-V plasty to correct telecanthus and epicanthus. Ptosis correction resulted well in separate sittings.

show abstract

Surgical strategy for congenital blepharophimosis syndrome

Cited by 11 publications

References 20 publications

Single stage surgery for Blepharophimosis syndrome

Single stage surgery for Blepharophimosis syndrome

Surgical outcome of epicanthus and telecanthus correction by C-U medial canthoplasty with lateral canthoplasty in treatment of Blepharophimosis syndrome

Surgical outcome of blepharophimosis syndrome: Double vs single stage

Contact Info

Product

Resources

About