Sweet syndrome: long-term follow-up of 138 patients

Marcoval, J.; Martín-Callizo, C.; Valentí-Medina, F.; Bonfill-Ortí, Montserrat; Martínez-Molina, L.

doi:10.1111/ced.12899

Cited by 36 publications

(30 citation statements)

References 14 publications

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“…In this respect, pain or tenderness was only reported in 26 % of patients studied by Marcoval et al. (36/138 patients) , and in 43 % of individuals studied by Rochet et al. (33/77) .…”

Section: Discussionmentioning

confidence: 88%

Sweet's syndrome: diagnostic criteria revisited

Nofal

Abdelmaksoud

Amer³

et al. 2017

J Deutsche Derma Gesell

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Summary The diagnosis of Sweet's syndrome (SS) is based on a set of criteria that requires the presence of two major and at least two minor criteria. In some cases, however, the diagnosis is not as straightforward due to the absence of certain criteria. The objective of the present study was to review the clinical, histopathological, and laboratory features of the current diagnostic criteria for SS, and to evaluate their validity in the cases reported in the literature as well as in 40 patients treated at our institution. Our comprehensive review of the current criteria for SS reveals that the two major criteria have been consistently present in all cases – including ours – since the first description of SS in 1964. With regard to the minor criteria, on the other hand, there has been marked variability between different studies, and many cases failed to fulfill the requirement of showing two minor criteria. In order to simplify the diagnosis, avoid misdiagnosis, and allow for prompt treatment, we propose two sets of revised diagnostic criteria for SS. The first set comprises constant clinical and histopathological features that must be present and are by themselves sufficient for the diagnosis of SS to be established. The second set includes variable features whose absence does not warrant ruling out SS.

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“…In this respect, pain or tenderness was only reported in 26 % of patients studied by Marcoval et al. (36/138 patients) , and in 43 % of individuals studied by Rochet et al. (33/77) .…”

Section: Discussionmentioning

confidence: 88%

Sweet's syndrome: diagnostic criteria revisited

Nofal

Abdelmaksoud

Amer³

et al. 2017

J Deutsche Derma Gesell

View full text Add to dashboard Cite

show abstract

“…The prognosis in SS is variable, and some patients achieve complete resolution of symptoms and skin lesions without any treatment (such as in drug-related SS after removal of the offending agent) while other patients’ symptoms persist for weeks to months, few ending in death 9 10. The skin lesions in malignancy-associated SS can occur at any time before, during or after the diagnosis of cancer.…”

Section: Discussionmentioning

confidence: 99%

An atypical presentation of Sweet’s syndrome in a myelofibrosis patient

Thebo¹,

Tummala

Nassereddine

et al. 2019

BMJ Case Rep

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A 46-year-old man with no significant medical history presented to haematology with symptoms of fatigue, dyspnoea on exertion and weight loss. Physical examination revealed a lesion on the right shin and splenomegaly. Labs were significant for leucocytosis with immature components, thrombocytosis and 3% peripheral blasts on smear. A bone marrow biopsy confirmed a diagnosis of myelofibrosis (MF). Dynamic International Prognosis Scoring system was 2. He was started on ruxolitnib, with decitabine added subsequently prior to definitive therapy with an allogenic haematopoietic stem cell transplant. His course with decitabine was complicated with febrile neutropaenia with multiple tender erythematous plaques unresponsive to antibacterial and antifungal coverage. A skin biopsy showed neutrophilic dermatitis, consistent with a diagnosis of Sweet’s syndrome (SS) and empirical treatment with glucocorticoids was initiated resulting in resolution of symptoms. This report reviews the literature for cases of SS in the setting of MF.

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“…1 Systemic symptoms such as fever, fatigue, and arthralgia often accompany these cutaneous findings. 1,2 Although the pathophysiology has not been fully elucidated, this syndrome frequently is associated with infections, especially upper respiratory illnesses; medications; and malignancies. Among cases of malignancy-associated Sweet syndrome, hematologic malignancies, particularly acute myeloid leukemia and myelodysplastic syndrome, are more common than solid organ malignancies.…”

Section: The Diagnosismentioning

confidence: 99%