Symptomatic congenital aortic stenosis in the first year of life

Incidental Diagnosis of the Unicuspid Aortic Valve with Ascending Aortic Aneurysm in an Asymptomatic Adult

“…The UAV was divided into 2 morphologic categories: one is the pin-hole shaped acommissural UAV, and the other is a slit-shaped unicommissural UAV 5). The acommissural UAV is usually accompanied by severe stenosis, therefore symptoms tend to be present at birth, and many patients undergo surgical intervention for severe stenosis during their infancy or childhood 6). The unicommissural form usually brings relatively larger orifice than acommissural form, thus it can be remained asymptomatic and hemodynamically stable until adulthood, which was the case in our patient.…”

Symptomatic unicuspid aortic valve

“…The acommissural type has a central pinhole-shaped opening and presents with symptoms that require intervention in infancy and childhood 5. In the unicommissural UAV, as in our patient, the valve has a slit-like opening 1.…”

An Adult Case of Unicommissural Unicuspid Aortic Valve Diagnosed Based on the Intraoperative Findings

“…Acommissural UAV presents with severe AS from the early stage (4); it is often associated with symptoms of left heart failure (5) and often requires invasive treatment from the neonatal period (4,16). On the other hand, unicommissural UAV which has one commissure with two rudimentary commissures with a broader valvular area, as in our patient, than that in acommissural UAV, is often asymptomatic until 30-50 years of age (17, 18).…”

“…This condition is divided into acommissural and unicommissural types; the former exhibits severe valve dysfunction and requires treatment from the neonatal period through childhood (3,4). On the other hand, the unicommissural type often remains asymptomatic until adulthood.…”