2017
DOI: 10.1155/2017/5032630
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Systemic Cystic Angiomatosis Mimicking Metastatic Cancer: A Case Report and Review of the Literature

Abstract: Systemic cystic angiomatosis is a rare benign disorder due to the maldeveloped vascular and lymphatic system with less than 50 cases reported in literature so far. We report here a case of systemic cystic angiomatosis (SCA) with multisystem involvement affecting the neck, thyroid, thoracic cavity, and skeletal system. The patient initially presented in her 4th decade of life with isolated lymphangioma in the neck requiring surgery. However, she experienced full-blown manifestations of SCA in her 6th decade whi… Show more

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Cited by 7 publications
(10 citation statements)
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“…Our patient presented in middle age, hence, a metastatic disease with multiorgan involvement was the first possibility kept as differential, and the main aim of multiple diagnostic tests was to rule out the same. A similar case reported by Kumar et al [4] considered metastatic disease due to multi-organ involvement; however, post the biopsy, turned out to be SCA.…”
Section: Discussionmentioning
confidence: 54%
“…Our patient presented in middle age, hence, a metastatic disease with multiorgan involvement was the first possibility kept as differential, and the main aim of multiple diagnostic tests was to rule out the same. A similar case reported by Kumar et al [4] considered metastatic disease due to multi-organ involvement; however, post the biopsy, turned out to be SCA.…”
Section: Discussionmentioning
confidence: 54%
“…Чаще всего это селезенка, на втором месте -легкие и плевра. Реже выявляются кисты печени и/или хилоторакс, что сопровождается плохим прогнозом [1,2,8].…”
Section: поражение внутренних органовunclassified
“…У детей КА приходится дифференцировать с гистиоцитозом из клеток Лангерганса, болезнью Горхема-Стаута, реже с метастатическим поражением костей; у взрослых -с миеломной болезнью и костными метастазами [1][2][3].…”
unclassified
“…3 Other sites include liver, kidneys, skin, soft tissue, lungs, and pleura. 2 The characteristic imaging appearance of the skeletal lesions include well-defined intramedullary cysts, a sclerotic peripheral rim, a preserved bony cortex, and no periosteal reaction. 4 A few cases of lytic bone lesions have also been described.…”
mentioning
confidence: 99%
“…4 A few cases of lytic bone lesions have also been described. 2,3 The sclerosing form is more commonly seen in elderly patients and the lytic lesions more commonly seen in younger patients. 2 Histologically, lesions are characterized by cystic or dilated vascular spaces lined by flat endothelial cells.…”
mentioning
confidence: 99%