The evolution of cerebrovascular changes in Köhlmeier-Degos disease: An 11-year follow-up case report

Clinico-Pathological Features in Köhlmeier–Degos Disease with Cutaneous and Neurological Involvement

“…Uncommonly, neurological features can precede or occur simultaneously with skin lesions. [ 4 ] Any part of the neuraxis can be affected and the clinical manifestations correspond to the site of involvement. Our patient manifested with neurological and ophthalmological features in the form of seizures, quadrantanopia, and multifocal brain lesions, which were secondary to vasculopathy of the leptomeningeal and cortical vessels.…”