The "harlequin" sign and congenital Horner's syndrome.

Morrison, Daniel R.; Bibby, K; Woodruff, Geoffrey

doi:10.1136/jnnp.62.6.626

Cited by 48 publications

(41 citation statements)

References 9 publications

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“…Blefaropitozis, miyozis, fasiyal anhidrozis ve iris hipokromisi klinik olarak Horner sendromu olarak tanımlanmaktadır 4,5 …”

Section: Discussionunclassified

Hemifasiyal Atrofinin Eşlik Ettiği Harlequin Sendromu

Polat¹,

Tuğ²,

Atasoy³

et al. 2012

Turkderm

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ÖzetHarlequin sendromu, yüzün bir yarısına sınırlı sıcaklık, emosyonel nedenler ve egzersiz ile flashing ve terlemenin olduğu otonomik bir sendromdur. Fasiyal flashing ve terleme "Harlequin işareti" olarak adlandırılır. Bu nadir özellik, "Harlequin işareti", yüzün flashing gerçekleşmeyen tarafında pre ya da postgangliyonik düzeyde lokalize bir servikal sempatik defisit nedeniyle lokal bir otonomik disfonksiyon gerçekleşmesidir. Konjenital Horner sendromuna neden olan bir lezyonun (pregangliyonik ya da postgangliyonik) muhtemel anatomik bölgesi belirlenmeye çalışıldığında görülebilir. Harlequin sendromu birkaç diğer sendromla da örtüşmektedir. Parry-Romberg sendromu etyolojisi bilinmeyen nadir klinik bir durumdur. Progresif hemifasiyal atrofi olarak da tanımlanır. Asimetrik fasiyal flashing ve terlemesi, ve yüzünün sağ yanında hemifasiyal atrofisi bulunan 9 yaşında erkek çocukta, fasiyal flashing ve terleme egzersiz, ısı artışı, ve emosyonel nedenler ile artmaktaydı. Sum maryHarlequin syndrome is an autonomic syndrome of heat, emotion and exercise induced flushing and sweating limited to one side of the face in combination with impairment of sweating and flushing on the contralateral side. Facial flushing and sweating has been named the "Harlequin Sign". This rare feature, "Harlequin Sign", represents a local autonomic dysfunction due to a cervical sympathetic deficit located at the pre or postganglionic level on the non-flushing side. Harlequin syndrome overlaps with several other syndromes. Parry-Romberg syndrome is a rare clinical entity of an unknown etiology. It is also described as progressive hemifacial atrophy. We report a nine-years old Turkish boy with asymmetrical facial sweating, flushing and hemifacial atrophy on the right side of his face.

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“…Blefaropitozis, miyozis, fasiyal anhidrozis ve iris hipokromisi klinik olarak Horner sendromu olarak tanımlanmaktadır 4,5 …”

Section: Discussionunclassified

Hemifasiyal Atrofinin Eşlik Ettiği Harlequin Sendromu

Polat¹,

Tuğ²,

Atasoy³

et al. 2012

Turkderm

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“…Anhidrosis results in facial flushing and dryness of the affected skin [4]. While lighter skinned subjects may demonstrate flushing on the affected side, it is almost impossible to demonstrate facial flushing in a majority of the dark skinned Indian population.…”

Section: Discussionmentioning

confidence: 99%

Minor’s Test: Objective Demonstration of Horner’s Syndrome

Sriraam

Sundaram

Ramalingam

et al. 2015

Indian J Otolaryngol Head Neck Surg

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To highlight the Minor's test, which is useful in demonstrating anhidrosis of Horner's syndrome. A 39 year old female presented to us with a slow growing neck swelling which was provisionally diagnosed as a probable case of cervical sympathetic chain (CSC) Schwannoma. Intra operatively, the mass was found arising from the CSC which was sacrificed. Post operatively, Horner's syndrome was expected, but was difficult to demonstrate clinically. On performing the Minor's test, the presence of anhidrosis, and thus Horner's syndrome was confirmed. Minor's test is a simple objective test to demonstrate Horner's syndrome, especially because diagnosis from the eye signs can be difficult.

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“…In pediatric patients with Horner syndrome, impaired facial flushing may be more apparent than anhidrosis [5].…”

Section: Introductionmentioning

confidence: 99%

Clinical Presentations of Pediatric Horner Syndrome

Smith¹,

Rathore²,

Suh³

2017

OJOph

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Purpose: To understand the multiple signs of Horner syndrome and to recommend protocols for pediatricians to obtain an accurate diagnosis of Horner syndrome. Methods: The medical records of 17 pediatric patients with Horner syndrome, neonates to eighteen years of age, were collected and analyzed. Data recorded included age, presenting symptoms, other medical history, allergies, medications, pupil size, presence of anhidrosis, and presence of ptosis. From the available pupil sizes, average degree of anisocoria was calculated. Results: All 17 patients had other clinical findings of Horner syndrome in addition to anisocoria. On initial evaluation, 100% had ptosis and 25% had anhidrosis. Of the available pupil size data, the average level of anisocoria was 2.06 mm, with a standard deviation of 1.17 mm. Conclusion: Physicians are reminded to measure pupil size to determine the degree of anisocoria when present, as it may help distinguish benign conditions from underlying pathology. Educating pediatricians on measurement of anisocoria and additional signs of Horner syndrome will help with proper referral patterns.

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The "harlequin" sign and congenital Horner's syndrome.

Cited by 48 publications

References 9 publications

Hemifasiyal Atrofinin Eşlik Ettiği Harlequin Sendromu

Hemifasiyal Atrofinin Eşlik Ettiği Harlequin Sendromu

Minor’s Test: Objective Demonstration of Horner’s Syndrome

Clinical Presentations of Pediatric Horner Syndrome

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