The Hemarthrosis-Simulating Knee Model: A Useful Tool for Individualized Education in Patients with Hemophilia (GEFACET Study)

Abstract

Background Hemophilic arthropathy is a major complication in patients with severe hemophilia. A plastic knee model has been developed for the therapeutic education of patients to promote improved care management and self-treatment skills. The objective of this study was to evaluate the impact of this hemarthrosis-simulating artificial knee (HSAK) on patients’ knowledge of their disease and its treatment. Methods In this observational study, the impact of HSAK was assessed during individualized education in patients with severe/moderately severe hemophilia A or B at seven hemophilia treatment centers in France. Participants provided written informed consent and completed questionnaires to assess knowledge of their disease (score range: 0–7) and knowledge of their treatment (score range: 0–4). Questionnaires were completed before, immediately after and 6 months after HSAK use. The scores obtained before and after the use of the HSAK were compared. Results The participants comprised 32 children, 29 teenagers, and 31 adults. The mean (SD) disease knowledge score increased significantly in all age groups of patients from 4.5 (2.0) to 5.9 (1.5; p<0.001) immediately after the training and remained unchanged at 6 months. Mean (SD) treatment knowledge scores were unchanged, but Wilcoxon signed rank testing showed a significant increase after the training course that was maintained at 6 months in children and teenagers. Conclusion These findings suggest that an individualized training course can enhance the understanding of hemophilia in patients of all ages, especially in children and teenagers, and that the HSAK may assist in improving patients’ management of their disease.

Hemophilia Patient Experience in a Physical Therapy-Guided Health Education Intervention: A Mixed-Method Design

“…Phadnis et al determined the effect of a health education intervention on the parents of people with hemophilia, who increased their knowledge of the disease and its management afterwards [ 45 ]. Health education is also useful to increase the knowledge about knee replacement in hemophilia, as found by Le Dore et al, especially in children and adolescents [ 46 ]. Similar data were obtained by Breakey et al in their study after an online self-management intervention for adolescents dealing with hemophilia, who were also prone to recommend the intervention to others [ 47 ].…”

Diagnostic and treatment methods of skeletal symptoms of haemophilia and education of patients regarding the disease – review study

“…French scientists developed a plastic knee model to educate patients with severe haemophilia about the major complication -haemophilic arthropathy [17]. They aimed to improve care management and selftreatment skills in both adults and children using hemarthrosis-simulating artificial knee.…”