The Incidence of Protrusio Acetabuli in Marfan's Syndrome and Its Relationship to Bone Mineral Density

Protrusio Acetabuli in Marfan Syndrome: Age-Related Prevalence and Associated Hip Function

“…Others have discussed combining triradiate physeal closure with a valgus intertrochanteric osteotomy to prevent worsening of protrusio 14 . In contrast, the only previously reported screening study for protrusio in individuals with Marfan syndrome, albeit one that involved only twenty-one patients, demonstrated no correlation between the presence of protrusio radiographically and clinical symptoms 6 .…”

“…n previous studies, the radiographic prevalence of protrusio acetabuli in patients with Marfan syndrome has ranged from 31% to 100%, but the largest of those series included only twenty-two patients [6][7][8] . The present study of a much larger population of patients with Marfan syndrome demonstrated a somewhat lower prevalence of 27% according to the criteria of Steel 8 and of only 16% according to the criteria of Armbuster 16 .…”

“…Since then, others have reported protrusio in small populations of patients with Marfan syndrome [6][7][8] . The presence of protrusio is now considered to be one of the skeletal criteria for a clinical diagnosis of Marfan syndrome according to the most recent Gent nosology 9 .…”

Protrusio Acetabuli in Marfan Syndrome<sbt aid="1084987">History, Diagnosis, and Treatment</sbt>

“…Since its recognition by Steel, many authors have stressed the importance of protrusio acetabuli in Marfan syndrome, which has a reported prevalence of 31% (in twenty-one patients 26 ) and 100% (in twenty-two patients 27 ). The deformity was accepted for inclusion in the International Nosology of Heritable Disorders of Connective Tissue 28 , Berlin, as a diagnostic manifestation of Marfan syndrome, although at that time it was regarded as less specific.…”

“…5)-is an indication of the integrity of the cortical quadrilateral plate of the pelvis. Others thought that this parameter alone is not accurate for determining true protrusio acetabuli and concluded that the best single radiographic indicator of protrusio acetabuli is the crossing of the acetabular and the iliopectineal line 26 -i.e., the cortical ridge forming the lower boundary of the greater pelvis. Others thought that this parameter alone is not accurate for determining true protrusio acetabuli and concluded that the best single radiographic indicator of protrusio acetabuli is the crossing of the acetabular and the iliopectineal line 26 -i.e., the cortical ridge forming the lower boundary of the greater pelvis.…”