The Life‐expectancy of Persons With Cerebral Palsy

Abstract

SUMMARY Survival rates for persons with cerebral palsy were calculated using information front a population‐based registry which has been collecting data since 1952. The 30‐year survival rate approximates 87 per cent. Adverse factors affecting survival are the type of cerebral palsy (spastic quadriplegia having the worst prognosis), epilepsy and severe or profound menial retardation. The length of time over which the data were collected precludes estimating survival time beyond 30 years. RÉSUMÉ Espérame de vie chez, les IMC/1MOC Les taux de survie chez les IMC/IMOC ont été calculés à partir des informations de registres dcar;état‐civil recueillies depuis 1952. Le taux de survie à ans est approximativement de 87 pour cent. Les facleurs négatifs affectanl la survie sont le type dcar;alleinte (les quadriplégic's spastiques ont le plus mauvais pronostic). lcar;épilepsie et lcar;arriération mentale sévére ou profonde. La période durant laquelle les données ont été recueillies ne perniet pas de calculer une espérance de vie au delà de 30 ans. ZUSAMMENFASSUNG Lebenserewartung; von Personal mit Cerebralparese Die Überlebensratcn von Personen mit Cerebralparese wurden anhand eines Registers, in dem seit 1952 Daten gesammelt worden waren, berechnet. Die 30‐Jahre‐Überlebensrate entspricht etwa 87 prozent. Fakiorert, die das Überleben negativ beeinflussen, sind bestimmte A.nen der Cerebralparese (wobei die spastische Tetraplegie die schechtestc Prognose hat). Epilepsic und schwere geistige Relardierung. Die Zeitspanne, in der die Daten gcsammelt wurden. Schlietßt die Beurteilung einer Überlebenszeit von mehr als 30 Jahren aus. RESUMEN Expeclativas de villa de persomts con paralisis cerebral Se calculó el porcentaje de supervivencias de personas con paralisis cerebral utilizando la information suministrada por un registro de una población base, cuyos datos se habia recogido a partir tie 1952. El porcentaje de supervivencia a los 30 años de edad era aproximadamente del 87 por ciento. Los factores que afectan negalivamente la supervivencia son ciertos tipos de paralysis cerebral (la que tiene peor pronoslieo es la cudriplejia espàstica). la epilepsis y un retraso mental profundo o grave. El largo tiempo durante el cual se recogieron los datos. impide hacer la estimación más allá de los 30 años.

The epidemiology of cerebral palsy in British Columbia.

“…They found that approximately 85% of children with severe four-limb cerebral palsy survived to 15 years of age, consistent with other studies (Hutton et al, 1994;Crichton et al, 1995;. The authors concluded that 15% of children with severe cerebral palsy died in childhood, suggesting that children with bilateral spastic cerebral palsy involving all four limbs are at a higher risk of mortality before they reach adolescence.…”

Life expectancy in pediatric patients with cerebral palsy and neuromuscular scoliosis who underwent spinal fusion

“…Some of these variables, such as ambulatory and cognitive ability, which were not found to be significant predictors for survival, are heavily influenced by the very small numbers of ambulatory children and the very few individuals with high level cognitive function in our study group. Based on previous studies (Evans et al 1990;Crichton et al 1995;Eyman et al 1990Eyman et al , 1993Hutton et al 1994Hutton et al , 2000Plioplys et al 1998;Strauss et al 1998), large populations that include more high-functioning individuals demonstrate these as significant factors. However, few of these less involved patients develop severe scoliosis.…”

“…Crichton et al (1995) analyzed the data from the CP registry in British Columbia, Canada, and reported a mean 30-year survival rate of at least 87%, varying from 95% in patients with hemiplegia or monoplegia to 83.5% in those with quadriplegia having the worst prognosis. The most significant determinants for reduced life expectancy in pediatric patients with CP are the coexistence of other significant disorders such as respiratory malfunction, epilepsy, feeding disorders (particularly in patients requiring gastrostomy or nasogastric tube feedings), the degree of neurological involvement, the presence of severe cognitive abnormality, and the level of ambulatory disability (Evans et al 1990;Eyman et al 1990Eyman et al , 1993Hutton et al 1994Hutton et al , 2000Crichton et al 1995;Anderson 1996;Plioplys et al 1998;Strauss et al 1998). Respiratory disease, especially pulmonary infection, seems to be the predominant cause of death, specifically among individuals with mental retardation (Tarjan et al 1968, Chaney et al 1979, Eyman et al 1990).…”

“…CP is probably the most common neurological disease that causes permanent physical disability in childhood (Hutton et al 1994(Hutton et al , 2000, but there is limited information on the predicted survival rate for this group of patients (Nelson et al 1994, Strauss et al 1998) even though affected individuals are assumed to have lower survival rates than the general population (Crichton et al 1995). Life expectancy in patients with CP after the development of scoliotic deformities or after surgical correction of scoliosis has not been reported.…”

Prognóstico motor e perspectivas atuais na paralisia cerebral

“…Os níveis de sobrevida para pacientes com PC têm sido calculados usando informações de registros de dados da população colhidos desde 1952 20 . Aproximadamente 87% das pessoas com PC sobrevivem até os 30 anos 21 e quase 85% dos que passam dos 20 anos sobrevivem até os 50 anos 22 .…”