The near complete tracheal ring deformity

Faust, Russell A.; Stroh, Brandon C.; Rimell, Frank L.

doi:10.1016/s0165-5876(98)00100-1

Cited by 29 publications

(9 citation statements)

References 20 publications

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“…These lesions are a rare anomaly in which the normal C-shaped tracheal cartilage is fused posteriorly, thus replacing the normal posterior membranous portion of the trachea. 3 However, in our case, the lesion was left-sided and not originating from the posterior wall of the trachea. If long segmental congenital tracheal stenosis with complete tracheal rings occurs, it presents as a lifethreatening and difficult to manage airway problem, usually manifesting early in life as severe respiratory distress.…”

Section: Iatrogenic Injury Of the Airwayscontrasting

confidence: 48%

Iatrogenic injury of the airways

Özdemir

Yeşil

Brown

2021

Pediatric Pulmonology

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Section: Iatrogenic Injury Of the Airwayscontrasting

confidence: 48%

Iatrogenic injury of the airways

Özdemir

Yeşil

Brown

2021

Pediatric Pulmonology

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“…Complete tracheal rings by themselves are rare and usually present in the first year of life [13]. However, in a retrospective study by Backer et al 15% out of their 71 patients with tracheal stenosis had the combination of complete congenital tracheal rings and unilateral lung agenesis or severe hypoplasia [14].…”

Section: Discussionmentioning

confidence: 99%

Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement

Agrawal

Patri

Kalavakunta

2016

Case Reports in Pulmonology

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Congenital lung agenesis is an extremely rare condition with an estimated prevalence of 34 in 1,000,000 live births. It is often associated with other congenital malformations of the skeletal, cardiovascular, urogenital, and gastrointestinal systems. We discuss the case of a 5-month-old who presented with increasing stridor over 1 month. Imaging revealed right lung agenesis, complete dextromalposition of heart, and compression of distal trachea. An intrathoracic saline tissue expander was placed which marked improved distal tracheal stenosis. In patients who are symptomatic it becomes imperative to perform surgeries to increase survival as was the case in this patient.

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“…The former were first described in 1897, and up until 1998, less than 100 cases have been reported, with only 4 cases of near-complete tracheal rings reported. Faust et al reported the first case of long-segment, near-complete tracheal ring deformity and long-segment anterior fusion of the cartilage rings in a living infant with a diagnosis of Pfeiffer's syndrome [11]. Both complete and nearcomplete tracheal rings may be treated conservatively or surgically.…”

Section: Discussionmentioning

confidence: 99%

Subglottic Ductal Cysts Associated with Complete Tracheal Ring Deformity: Coexistence of Two Rare Airway Abnormalities with Fatal Outcome

et al. 2004

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Subglottic cysts are rare and may cause airway obstruction. Most cases are acquired secondary to endotracheal intubation, even short-term, particularly in the premature neonate. Complete tracheal rings are rare anomalies associated with tracheal stenosis. To our knowledge, the two have not been reported coexisting. A 16-month-old ex-premature boy was found unresponsive, with his tracheostomy tube dislodged. Tracheomalacia, subglottic stenosis, and a laryngeal cyst had been diagnosed shortly after birth, and the cyst was surgically treated at that time. At autopsy, a complete tracheal ring was noted in the subglottic region, above the tracheostomy site, and the tracheal diameter was markedly decreased in this area. In addition, multiloculated cysts were present at that level, arising from both anterolateral tracheal walls. These completely occluded the airway. To our knowledge, this is the first case of a combination of tracheal ring anomaly and subglottic cysts. Pediatric pathologists must be aware of iatrogenic lesions associated with care of the premature neonate, particularly as the age of viability continues to decrease.

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The near complete tracheal ring deformity

Cited by 29 publications

References 20 publications

Iatrogenic injury of the airways

Iatrogenic injury of the airways

Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement

Subglottic Ductal Cysts Associated with Complete Tracheal Ring Deformity: Coexistence of Two Rare Airway Abnormalities with Fatal Outcome

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