Purpose. To familiarize gynecologists with the clinical presentation, diagnosis and basic principles of treatment of thoracic endometriosis (TE).Materials and Methods. The article presents a review of publications based on the results of search in electronic resources PubMed, Elibrary, EMBASE. The own clinical observation of the patient with TE is also presented.Results. The clinical picture of TE can be different, in many patients it is asymptomatic. The typical symptom of TE is menstrual cycle-related, usually right-sided pain in the thoracic, scapular or shoulder area. Chest X-rays, computed tomography (CT), magnetic resonance imaging (MRI) and bronchoscopy are used in diagnosis. The gold standard for definitive diagnosis and effective treatment is video-assisted thoracoscopic surgery (VATS). As with pelvic disease, the first-line therapy for TE is medication to suppress ovarian steroid hormone production. Surgical treatment should be considered in patients with refractory or recurrent TE and in acute life-threatening conditions.Conclusion. Management of patients with thoracic endometriosis requires an interdisciplinary approach involving gynecologists and thoracic surgeons.