The rare congenital anomaly of pulmonary sequestration experience and review of literature

Abstract

Objective Pulmonary sequestration is rare lung anomaly which had very major theories of origin. The aim of this study was to treat this rare congenital anomaly, pulmonary sequestration, which was not diagnosed of preoperatively, in our centre. Methods A retrospective analysis of 10 cases of pulmonary sequestration operated at the centre between 2000 and 2010. A review of the extralobar and intralobar types of sequestration is discussed. All patients were not diagnosed preoperatively. Results Pulmonary sequestration is found more commonly in women (6 patients). In all patients, the diagnosis was made by exploratory thoracotomy. Six patients had intralobar (one was apical) and 4 were extralobar (one apical). Lobectomy for intralobar and sequestrectomy for extralobar sequestration were performed.Conclusions Although rare, some radiological features are sufficiently suggestive of diagnosis of pulmonary sequestration. We believe that pulmonary sequestration should be considered when intrathoracic masses cannot be differentiated through invasive and non-invasive evaluation. In difficult cases methods such as aortagraphy, doppler angiography and Magnetic Resonance (MR) angiography may be used.

Rare case of haemoptysis

“…It is interesting that the diagnosis of sequestration in all 10 patients was made intraoperatively 5. The preoperative diagnosis on chest CT was lung mass in six cases, posterior mediastinal mass in two cases, lung cyst in one case and empyema in one case 5. Furthermore, two cases of pulmonary sequestration were reported in patients aged 58 and 52 years 4 7.…”

“…[3–7]. In a series of 10 adult patients with a mean age of 35 years, symptoms included cough, haemoptysis, chest pain and back pain 5. It is interesting that the diagnosis of sequestration in all 10 patients was made intraoperatively 5.…”

“…In a series of 10 adult patients with a mean age of 35 years, symptoms included cough, haemoptysis, chest pain and back pain 5. It is interesting that the diagnosis of sequestration in all 10 patients was made intraoperatively 5. The preoperative diagnosis on chest CT was lung mass in six cases, posterior mediastinal mass in two cases, lung cyst in one case and empyema in one case 5.…”

Inferior vena cava obstruction as a rare manifestation of bronchopulmonary sequestration

“…3 BPS is divided into two categories based on pleural coverage: intralobar sequestration (ILS) and extralobar sequestration (ELS). 1 In 1947, Pryce classified ILS into three types based on its arterial supply: (i) systemic arterial supply to a normal segment; (ii) systemic arterial supply to a sequestered segment, as well as a normal segment; and (iii) systemic arterial supply only to a sequestered segment. In some cases, it can be acquired.…”

“…1 BPS is symptomatic in childhood, but can remain silent until adulthood. 1 BPS is symptomatic in childhood, but can remain silent until adulthood.…”