Thrombosed congenital extrahepatic portal vein aneurysm in an infant

Abstract

Extrahepatic portal vein aneurysm is extremely rare in infants. We report an infant with thrombosed congenital extrahepatic portal vein aneurysm demonstrated on US and CT. Follow-up US after 16 months showed complete regression of the portal vein aneurysm.

Feasibility and safety of non-operative management of portal vein aneurysms: a thirty-five year experience

“…13 One obvious concern for observant management is the potentially fatal risk of rupture and gastrointestinal bleeding. 6,21,22 However, the actual risk of these complications is essentially unknown due to the paucity of available long term follow up data and with only a handful of patients presenting with these complications. Some studies suggest visceral compression and spontaneous rupture occurring in approximately 10% of cases, 13,23,24 however, this was not observed in our cohort despite our encounter with large aneurysms and those complicated by thrombosis.…”

Portal Vein Aneurysm Treated With Trans-Jugular Intrahepatic Porto-Systemic Shunt

“…2 Aneurysmal rupture is rare due to the relatively low portal venous pressures, but risk increases in the setting of portal venous hypertension. 3,6,11 Portal vein thrombosis is more common, occurring in up to 20% of patients, and is almost always associated with abdominal pain when acute. 2 Acute portal vein thrombosis, particularly when extending to the superior mesenteric vein, carries risk of bowel ischemia or infarction.…”

A rare pediatric case of portal vein aneurysm thrombosis

“…Portal vein aneurysm (PVA) is a rare disorder, with only 200 cases recorded in the literature, in the form of clinical case reports or case series describing small numbers of patients, most of whom have been adults. [ 1 , 2 ] A portal vein diameter larger than 2 cm on ultrasound or computed tomography imaging is considered the definitive diagnostic criteria for PVA [3] , which is often detected accidentally in patients who present without symptoms or serious comorbidities. [ 1 , 2 ] Possible complications of PVA include thrombosis, aneurysm rupture, and portal hypertension, among which thrombosis is the most common complication.…”

“…[ 1 , 2 ] A portal vein diameter larger than 2 cm on ultrasound or computed tomography imaging is considered the definitive diagnostic criteria for PVA [3] , which is often detected accidentally in patients who present without symptoms or serious comorbidities. [ 1 , 2 ] Possible complications of PVA include thrombosis, aneurysm rupture, and portal hypertension, among which thrombosis is the most common complication. [1] Due to its rarity, the treatment of PVA and its complications remain controversial, with no specific guidelines established for this disorder.…”

“…[ 1 , 2 ] Possible complications of PVA include thrombosis, aneurysm rupture, and portal hypertension, among which thrombosis is the most common complication. [1] Due to its rarity, the treatment of PVA and its complications remain controversial, with no specific guidelines established for this disorder. [4] Our case was a 10-year-old child who suffered from PVA with thrombosis, which was initially misdiagnosed as a pancreatic head tumor.…”