When encountering a smooth-surfaced mass of uncertain origin, it is important to perform imaging studies before biopsy; inappropriate biopsy may cause facial nerve paralysis. 7,8 Computed tomography or magnetic resonance imaging is useful for diagnosis and decision-making about the surgical approach. 1,3,4,6 If EAC mass raises a suspicion of schwannoma, preoperative computed tomography or magnetic resonance imaging should be performed to explore tumor size, location, possible extension, and origin.In our present case, large schwannoma almost completely occluded the EAC and the patient reported a mild sensation of ear fullness. However, active treatment was chosen because we were of the view that conductive hearing loss and recurrent otitis externa caused by EAC obstruction would develop if the mass grew further. If a patient presents with symptoms attributable to a large mass in the EAC, surgical excision should be considered and pathological diagnosis is mandatory.The significance of the case is that schwannoma in the EAC is rare but should be included in the possible diagnosis of a cystic mass. If schwannoma is suspected, computed tomography or magnetic resonance imaging should be performed to explore tumor size, location, possible extension, and origin before excision. After excision, histopathological confirmation is mandatory. The prognosis after excision of EAC schwannoma is good.