Epididymal cysts in children are rare, and, as a rule, their detection is an incidental finding, the course is asymptomatic, the surgical treatment is not carried out. Isolated torsion of these cysts is extremely rare in both children and adults, causing acute pain syndrome and swelling of the scrotum. Due to its rarity and lack of specificity of clinical and echographic manifestations, this condition leads to a delay in the accurate diagnosis of the disease, which is carried out only intraoperatively. The rare case of combined testicular torsion and torsion of a large appendage cyst in a 12-year-old teenager is presented in the publication.