Tracheobronchomegalie Ou Syndrome De Mounier-Kuhn

Abstract

Mounier-kuhn Syndrome or The Tracheobronchomegaly is a rare condition characterized by marked dilatation of the trachea and the main bronchi. It is more common in males and diagnosed in the third and the fourth decades of life. Symptoms in MKS are nonspecific. Usually the patient present recurrent lower respiratory tract infection, chronic cough, and rarely with spontaneous pneumothorax. Patients are often diagnosed on CT scan, which shows large airways with sometimes the formation of diverticula in the major airways. We report the case of a patient who presented with aMounier-Kuhn Syndrome revealed by respiratory recurrent symptoms.

Tracheobronchomegaly (Mounier-Kuhn Syndrome) with CT and bronchoscopic correlation: A case report

“…Treatment of symptomatic patients is based on respiratory physiotherapy and the use of antibiotics during infectious exacerbations [28] . Bronchodilators and corticosteroids are used to control symptoms [2] . Our patient had a moderate form of the disease.…”

“…It is characterized by an important dilatation of the trachea and the proximal bronchi, responsible for recurrent respiratory infections [1] . Clinical signs are not very specific [2] . Radiological diagnosis is often easy on chest X-ray and computed tomography (CT) scan based on the measurement of the diameter or surface of the trachea and stem bronchi [3] .…”