Tracheal agenesis is a devastating congenital anomaly first described in 1900 by Payne. 1 In 1962 Floyd et al.2 classified tracheal agenesis into three types (Figs. 1, 2, and 3). One year later, Fonkalsrud et al. 3 attempted the first surgical correction of this anomaly. This attempt, as well as other interventions, have been unsuccessful in allowing any long-term survival.Eighty-seven cases have previously been identified in the world literature. This additional Floyd type III case typifies the problems of assessment and management of this fatal anomaly. A discussion of the embryology and associated congenital anomalies is presented. The clinical aspects of managing this abnormality are described along with previous attempts at surgical correction. Newer investigations may lead to a solution of this lethal anomaly.
CASE REPORTA full-term, 3300-gm girl was delivered by normal spontaneous vaginal delivery to a 23-year-old gravida 2, para 1 mother who had an uncomplicated pregnancy with a normalappearing ultrasound at 20 weeks. After delivery the child was noted to have respiratory distress with Apgar scores of 3 and 6 at 1 and 5 minutes. The infant was noted to have an absent cry. Attempt was made to intubate the infant without success. Saturations were maintained with the use of bag-valve mask. Attempts at intubation by the neonatology service were also unsuccessful, and the child was taken to the neonatal intensive care unit while being supported by bag and mask. The ototaryngology service was called, and after direct laryngoscopy revealed no subglottic opening, the infant was taken directly to the operating room. Further endoscopy at this time revealed essentially normal-appearing vocal folds with complete occlusion of the airway immediately in the subglottic area. A patent esophagus was identified posteriorly. A neck exploration was performed in an attempt to identify a tracheal rem-From the Divisions of Otolaryngology (Dr.