Introduction:Congenital coronary anomalies are a recognized cause of myocardial ischaemia and sudden cardiac death, especially among children and young adults. 1 The prevalence of congenital coronary anomalies has been estimated at approximately 0.85%-1% of general population and the incidence of coronary artery anomalies is 2% to 8% in patients with Fallot's tetralogy. 1-5 TOF is often lethal if untreated, it now has a good prognosis with timely surgical intervention. The best age for repair remains controversial but can be done at any age safely with low operative risk but should provide good relief of right ventricular outflow tract obstruction (RVOTO) to prevent progression of right ventricular (RV) hypertrophy. Proponents for primary neonatal repair cite factors such as prevention of time related end organ damage from cyanosis, removal of stimulus for RV hypertrophy and fibrosis, improved lung development (vascular and alveolar), avoidance of deleterious effects and risks of palliative shunts and psychosocial -economic issues. Surgical approach in patients having one coronary artery crossing the obstructed and hypertrophied right ventricular outflow tract (RVOT) is challenging and associated with increased operative mortality and morbidity. 3 Presurgical documentation of coronary artery anomalies is essential for the most appropriate surgical approach. Echocardiographic assessment, coronary angiography, CT angiogram or recently developed electrocardiographygated multidetector row CT (MDCT)-a noninvasive, accurately imaging technique to visualize the coronary arteries from their origin, course and termination and is superior to conventional coronary angiogram. 6,7 Various techniques have been described to establish the continuity between the right ventricle and the pulmonary artery. The type of surgical reconstruction is individualized depending on both the anatomy of the RVOT and the course of the coronary artery over it. Techniques for RVOT reconstruction include an oblique ventriculotomy, tailored ventriculotomy, two patch repair, translocation of the main pulmonary artery, transannular repair below a mobilized coronary artery and pulmonary homograft conduit. 8 We performed transventricular and transannular patchplasty with a monocusp after excision of septoparietal fibromuscular bands and anastomosis of LIMA to distal segment of sacrificed left anterior descending artery(LAD) in an adult patient. This corrective technique is appropriate in adult patients with anomalous non-tortuous coronaries which do not allow dissection and mobilization with the possibility of stress.
Tetralogy of Fallot with Anomalous Left Anterior