“…Symptomatic cases that manifested themselves for the first time in adulhood have been reported much less frequently [2,4], Some of these cases were most likely overlooked because of an unawareness of this malforma tion or they were misdiagnosed as other diseases even when they were symptomatic; this is what occurred the first time when symptoms appeared in the present case. It is very important to be aware of this condition for a cor rect diagnosis [1,4], Cardiovascular lesions were rarely associated with DAA but included tetralogy of Fallot [5], transposition of great arteries [5], ventricular septal defect [7], patent duc tus arteriosus [7] and traumatic rupture of the retro esophageal arch [8]. To our knowledge, the association of AR with DAA has not been previously reported, and it was not clear whether the association of AR in this case was incidental.…”