Ulnar Polydactyly and Ulnar Dimelia

Hiro, Matthew E.; Gottschalk, Hilton P.; Light, Terry R.

doi:10.1007/978-3-030-64159-7_21

Cited by 5 publications

(12 citation statements)

References 65 publications

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“…In addition to this complexity, the type and severity of postaxial polydactyly to some extent are related to ethnicity as well. It is more common in African populations with an incidence of one in every 100 to 300 live births compared to Caucasian children in which the incidence of postaxial polydactyly is one in every 1500 to 3000 live births [ 2 , 9 ]. In those of African descent, postaxial polydactyly tends to be bilateral in the majority of cases and is usually isolated and autosomal dominant [ 9 ].…”

Section: Discussionmentioning

confidence: 99%

“…It is more common in African populations with an incidence of one in every 100 to 300 live births compared to Caucasian children in which the incidence of postaxial polydactyly is one in every 1500 to 3000 live births [ 2 , 9 ]. In those of African descent, postaxial polydactyly tends to be bilateral in the majority of cases and is usually isolated and autosomal dominant [ 9 ]. In other populations, it tends to be unilateral and sporadic [ 9 ].…”

Section: Discussionmentioning

confidence: 99%

“…In those of African descent, postaxial polydactyly tends to be bilateral in the majority of cases and is usually isolated and autosomal dominant [ 9 ]. In other populations, it tends to be unilateral and sporadic [ 9 ]. Our case supports the common finding that ulnar polydactyly is isolated, but it is unusual in that it is unilateral ulnar polydactyly and there is no family history of note to suggest an autosomal dominant mode of inheritance.…”

Section: Discussionmentioning

confidence: 99%

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Complex Hand Polydactyly: A Case Report and Literature Review

Alzarmah¹,

Bhat²,

Nawwab³

2021

Cureus

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Polydactyly is a common congenital malformation in which extra digits are present in at least one extremity. It has various presentations, and it can be an isolated anomaly or part of other diseases. Most isolated polydactyly cases are sporadic and unilateral, but there is an increased incidence in some populations. Polydactyly is multifactorial and can occur in different forms. Its main line of treatment is surgery to improve cosmesis and functioning. In this report, we present a rare case of bilateral complex hand polydactyly in a one-year-seven-months old girl of African descent. She is otherwise healthy with no family history of malformations. The pattern is not consistent with any syndromic disease. She subsequently underwent surgical resection of the extra digits.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

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Complex Hand Polydactyly: A Case Report and Literature Review

Alzarmah¹,

Bhat²,

Nawwab³

2021

Cureus

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“…Postaxial polydactyly Type B involves the presence of a small, non-functioning supernumerary digit that is often pedunculated. 1 Most common among African-American children in whom the condition usually follows an autosomal-dominant inheritance pattern, it can also be seen in children of any race or ethnicity. 1,2 Suture ligation has been a common method of removing these digits and is performed using suture or vascular clip to tie off the digit, which then becomes necrotic and usually falls off.…”

Section: Introductionmentioning

confidence: 99%

“…1 Most common among African-American children in whom the condition usually follows an autosomal-dominant inheritance pattern, it can also be seen in children of any race or ethnicity. 1,2 Suture ligation has been a common method of removing these digits and is performed using suture or vascular clip to tie off the digit, which then becomes necrotic and usually falls off. 2 Families may be uncomfortable with the appearance of the digit until it falls off, and there are also risks of complications such as infection, a residual bump left on the ulnar border of the hand, and scarring.…”

Section: Introductionmentioning

confidence: 99%

Use of a “Fast, Feed, and Wrap” Technique with Local Anesthesia for In-Office Surgical Correction of Postaxial Polydactyly Type B in Infants

Gottschalk¹,

Garza²,

McMahon³

et al. 2022

Journal of the Pediatric Orthopaedic Society of North America

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Surgical correction of postaxial polydactyly type B has several potential advantages over the traditional approach of suture ligation. Benefits include achieving more cosmetic results, reduced risk of neuroma or bothersome scar, and decreased likelihood of needing a second procedure. Previous reports with small numbers of patients have described surgical polydactyly excision using local anesthesia only, either in the operating room or office setting. We now routinely perform these removals in the office using local anesthesia combined with a fast, feed and wrap (FFW) technique to improve the comfort of the patient and parents. Details and photos of this technique are provided, and we encourage those who still perform routine suture ligation to consider this method as a simple and effective alternative.

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A review of polydactyly and its inheritance: Connecting the dots

Bubshait

2022

Medicine

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Objective: This study collects what is known about the inheritance underpinnings of syndromic and non-syndromic polydactylies and highlights dactyly presentations with unknown genetic roots. This review summarizes the current information and geneticsenhanced understanding of polydactyly.Background: There is a frequency of 0.37 to 1.2 per 1000 live births for polydactyly, which is also known as hyperdactyly. It is characterized by the presence of extra fingers. Polydactyly is caused by a failure in limb development, specifically the patterning of the developing limb bud. The phenotypic and genetic variability of polydactyly makes its etiology difficult to understand. Preaxial polydactyly, central polydactyly (axial), and postaxial polydactyly are all examples of non-syndromic polydactyly (ulnar). An autosomal dominant disorder with varying penetrance that is mostly passed down via limb development patterning abnormalities.Method: A comprehensive search of MEDLINE/PubMed and other databases was followed by an evaluation of the relevant papers, with a particular focus on those published between 2000 and 2022.Results: Of 747 published article related to Polydactyly from MEDLINE/PubMed search, 43 were from the last 10 years and were the focus of this review. Conclusion:Polydactyly is one of the most frequent congenital hand malformations. PAP is more common than PPD, whereas central polydactyly is very uncommon.

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Ulnar Polydactyly and Ulnar Dimelia

Cited by 5 publications

References 65 publications

Complex Hand Polydactyly: A Case Report and Literature Review

Complex Hand Polydactyly: A Case Report and Literature Review

Use of a “Fast, Feed, and Wrap” Technique with Local Anesthesia for In-Office Surgical Correction of Postaxial Polydactyly Type B in Infants

A review of polydactyly and its inheritance: Connecting the dots

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