Three cases of choledochal cyst associated wIth Intrahepatic biliary dilatation are presented. Findings on sonographyIncluded a large cystic mass in the porta hepatis separate from the gallbladder;a dilated common hepatlc or common bile duct entering directly Into the cyst; and smaller cystic masses of dilated central intrahepatic ducts. The dIlatation of the central lntrahepatlc bile ducts was moderate In two patients and massive in one patient. All three patients underwent operation with lntraoperative cholangiography.Two patients had se@@@Tc IDA cholescintigraphywhich confirmed the Choledochal cyst, a dilatation of the biliary ductal system, is uncommon. Although the most common form of the disease is cystic or fusiform dilatation of the common bile duct, choledochal cysts with dilated intrahepatic bile ducts recently have been recognized with increasing frequency [1 , 2]. The diagnosis of choledochal cyst has been difficult to make preoperatively because the clinical picture may vary from the almost complete absence of symptoms to the manifes tation of a classic triad of right upper quadrant pain, mass, and jaundice. Invasive techniques such as intravenous cholangiography, arteriography, endoscopic retrograde cholangiopancreatography, and percutaneous transhepatic cholan giography have been used for diagnosis [3â€"5].Recently sonography has been suggested as having an important role in evaluating this entity [6â€"12]. We present three cases of choledochal cyst associated with intrahepatic biliary dilatation where an accurate preoperative diagnosis was made by combined B-mode and real-time sonography complemented by e9mTc IDA cholescintigraphy, thereby obviating more invasive diagnostic techniques in all three cases.
CaseReports
Case 1A 2-year-old girl was referred to Children's Hospital Medical Center because of recurrent lowerabdominal pain and vomitingfor 7 months.Initially,her pain wasthoughtto be due to intermittent ileocolic intussusception; however, barium enema on two separate occasions did not show any evidence of intussusception. Repeated liver function tests were normal. Abdominal sonography (fig. 1A) demonstrated an abnormal cystic mass with branching tubular structures in the hilum of the liver. A distended gallbladder was noted separate from the cystic mass. Smaller cystic structures were seen in the central part of the liver representing dilated intrahepatic bile ducts. A 99―Tc dimethyl-IDA scan (figs. 1B and 1C) demonstrated hepatic uptake at 10 mm and delayed filling and retention in the choledochal cyst at 21 hr after injection. Isotope activity in the intestine could not be clearly identified. The preoperative diagnosis of choledochal cyst with intrahepatic duct dilatation was confirmed at operation. In addition, marked narrowing of the distal common bile duct was