Ultrasonography of desmoplatic fibroma of the mandible; a case report.

Abstract

Desmoplastic fibroma (DF) is a very rare bone tumor, classified as a benign lesion. It might be locally a very aggressive tumor with a high rate of recurrence after surgical resection. We present a case of a 3-year and 6 month-old patient, with mandibular desmoplastic fibroma. The clinical, imaging, histological findings and surgical treatment are discussed and, also, a brief review of the literature of DF is presented. The purpose of this case report is to emphasize the particularity of the case, ultrasound findings and the main differential diagnostic of this rare bone tumor.

Desmoplastic Fibroma of the Mandible in an Infant: A Case Report

“…This finding is in agreement with Mohammadi et al (12) Due to the aggressive behavior of DF, different treatment protocols have been proposed. (13) Higher recurrence rate (37%-72%) of DF after enucleation and curettage was reported by Gersak et al (14) While Böhm et al, showed no recurrences after resection with wide surgical margins. (15) Radiotherapy is not recommended due to the lesion's potential for mutagenic transformation into fibrosarcoma.…”

Desmoplastic fibroma of the mandible: a rare gnathic bone tumor with a review of the literature

“…Anecdotal reports of successful use of radiotherapy in patients with DF are available, though these cases were of DF involving the lower limbs and not the gnathic bones 53 , 54. A wide range of complications have been described in cases of DF ranging from difficulty in mouth opening, extension into the adjacent soft tissue, perineural encasement, loosening of the overlying tooth, dysfunction of the temporomandibular joint, sinusitis, and nasal obstruction 1 , 8 , 13 , 22 , 23 , 25 , 27 , 28 , 32 , 36 , 41 , 42 , 44. All the complications are secondary to the aggressive nature of the tumor and the mass effect.…”