Undifferenziertes, embryonales Sarkom als seltene Ursache einer Leberruptur beim Erwachsenen

Abstract

This case report illustrates the possibility of an embryonal sarcoma being the reason for spontaneous rupture of the liver. The management of this case comprised primary tamponade, interventional embolisation of the feeding artery, and secondary resection under stable conditions.

Undifferentiated Embryonal Sarcoma of Liver

“… 4 Painless abdominal distension secondary to the hepatic mass as well as spontaneous rupture of the tumor leading to intraperitoneal hemorrhage in rapidly growing tumors has been reported. 9 For unclear reasons, the right lobe is known to be more commonly involved than the left lobe, although simultaneous involvement of both the lobes have also been reported. 4 , 5 Laboratory tests are of limited use as liver function can be normal or mildly deranged.…”

Surgical perspective on treatment of pediatric undifferentiated sarcoma of the liver

“…The emergency treatment in case of spontaneous or post biopsy tumor rupture is arterial embolization of the feeding artery [32,33] . Recent data supports that secondary tumor resection with preoperative chemotherapy is more successful than primary resection without an effective adjuvant regimen in this particular setting [31] .…”

“…Preoperative tumor rupture raises questions about recurrence as it can lead to inappropriate primary tumor resection [9] . Spontaneous tumor rupture was reported to occur in 6.5% of the patients [31] . The emergency treatment in case of spontaneous or post biopsy tumor rupture is arterial embolization of the feeding artery [32,33] .…”

Undifferentiated embryonal sarcoma of the liver treated with associating liver partition and portal vein ligation for staged hepatectomy in a young adult: A case report

“…Of primary liver tumors in children, the hepatoblastoma and the hepatocellular carcinoma are the most common, followed by the focal nodular hyperplasia and then the embryonal sarcoma. The undifferentiated embryonal sarcoma of the liver (UESL), firstly identified as an independent clinicopathologic type of sarcoma in 1978, is seen in about 2 % [[1], [2], [3]]. Typically, there is no pre-existing liver disease.…”