Une dilatation segmentaire uni ou pluri-focale des voies biliaires intra-hépatiques à l’échographie. Quelle conduite à tenir ?

Mp, Vullierme; Vilgrain,

doi:10.1016/s0221-0363(06)74030-6

Cited by 4 publications

(2 citation statements)

References 23 publications

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“…Ultrasound examination is very accurate in detecting intrahepatic stones, since they appear as heterogeneous and echoic foci centred on the intrahepatic ducts, or as a “comet-tail” artefact due to ultrasound reverberation (Fig 1) [19, 20]. The artefact is not mobile, as opposed to pneumobilia.…”

Section: Intrahepatic Lithiasismentioning

confidence: 99%

Hepatobiliary anomalies associated with ABCB4/MDR3 deficiency in adults: a pictorial essay

et al. 2013

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BackgroundABCB4/MDR3 gene variants are mostly associated with a peculiar form of cholelithiasis in European adults, currently referred to as low phospholipid-associated cholelithiasis (LPAC) syndrome.MethodsLPAC syndrome is a rare genetic disorder, characterised by the following clinical features: biliary symptoms before the age of 40, recurrence of the symptoms after cholecystectomy, and intrahepatic microlithiasis or intrahepatic hyperechogenic foci.ResultsImaging features associated with ABCB4/MDR3 mutations are not specific and correspond to a wide spectrum of biliary abnormalities. The main feature is the presence of intrahepatic lithiasis. Other uncommon presentations have been described, such as uni- or multifocal spindle-shaped dilatations of the intrahepatic bile ducts filled with gallstones, secondary sclerosing cholangitis, biliary cirrhosis, and intrahepatic cholangiocarcinoma.ConclusionThis review focuses on MR features related to ABCB4/MDR3 mutations.Main Messages• LPAC syndrome is characterised by intrahepatic microlithiasis or intrahepatic hyperechogenic foci.• Ultrasound examination is very accurate in detecting intrahepatic stones.• At MR imaging, LPAC syndrome is associated with various presentations.

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Section: Intrahepatic Lithiasismentioning

confidence: 99%

Hepatobiliary anomalies associated with ABCB4/MDR3 deficiency in adults: a pictorial essay

et al. 2013

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“…Elle représente moins de 1 % des dilatations kystiques congénitales des voies biliaires et correspond au type V de la classification anatomique de Todani et al [2]. La maladie de Caroli est dans 15 % des cas localisée à un seul lobe du foie, il s'agit du lobe gauche dans 92 % des cas [3,4].…”

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The role of surgery in localized form Caroli’s disease

Alami

Benamr

Mouslik

et al. 2010

J Afr Hepato Gastroenterol

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La maladie de Caroli est une dilatation kystique segmentaire congénitale des voies biliaires intrahépatiques. C'est une cause rare de cholestase chronique et de lithiases intrahépatiques. Nous rapportons deux cas de maladie de Caroli monolobaire gauche révélée par des poussées d'angiocholite atypique. Une hépatectomie gauche a été réalisée, d'emblée dans un cas, après des gestes chirurgicaux et endoscopiques infructueux dans l'autre. Le diagnostic préopératoire repose sur l'imagerie, mais seule l'étude anatomopathologique permet de le confirmer et de dépister une néoplasie. Le traitement logique de la maladie de Caroli monolobaire est la résection complète des régions atteintes qui peut être assurée avec succès par la résection hépatique. Mots clés Maladie de Caroli · Dilatation des voies biliaires intrahépatiques · HépatectomieAbstract Caroli's disease is a segmental congenital cystic dilatation of the intrahepatic biliary tree. It is a rare cause of chronic cholestasis and intrahepatic gallstones. We report two cases of Caroli's disease localized to the left half of the liver, revealed by recurrent atypical cholangitis. A left hepatectomy was performed at once in one case and after multiple unsuccessful endoscopic and surgical acts in the other case. The preoperative diagnosis was based on the imaging study, but only histopathology can confirm and track neoplasia. The logical treatment of the localized form of Caroli's disease is the complete resection of the affected lobe, which can be successfully achieved by partial hepatectomy.

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Les nouvelles possibilités d’exploration des voies biliaires en IRM : de l’imagerie morphologique à l’imagerie fonctionnelle avec perfusion de Mangafodipir Trisodium (Mn DPDP)

Laurent

Corby

Barbary

et al. 2007

Journal de Radiologie

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Une dilatation segmentaire uni ou pluri-focale des voies biliaires intra-hépatiques à l’échographie. Quelle conduite à tenir ?

Cited by 4 publications

References 23 publications

Hepatobiliary anomalies associated with ABCB4/MDR3 deficiency in adults: a pictorial essay

Hepatobiliary anomalies associated with ABCB4/MDR3 deficiency in adults: a pictorial essay

The role of surgery in localized form Caroli’s disease

Les nouvelles possibilités d’exploration des voies biliaires en IRM : de l’imagerie morphologique à l’imagerie fonctionnelle avec perfusion de Mangafodipir Trisodium (Mn DPDP)

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