Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Abstract

The unilateral absence of pulmonary artery (UAPA) is a rare congenital cardiovascular malformation, which is asymptomatic and easy to be ignored in early stage. A large number of complications may occur in the later stage. Therefore, early diagnosis and treatment is of great significance. The imaging data of 49 patients with UAPA discovered and confirmed clinically by the echocardiography in our hospital are analyzed. The results show that left pulmonary artery absence is more common (55%) and most of them are associated with other cardiovascular malformations (92%). Atrial septal defect and patent foramen ovale were most common in 56%. In which the absence of isolated pulmonary artery was 8% (4/49), and the absence of right pulmonary artery was 75% (3/4). Especially in the patients with tetralogy of Fallot, 77% (5/9) of them miss the diagnosis of UAPA. This suggests that doctors and sonographers should pay attention to the development of pulmonary artery bifurcation and left and right branches in multi-section, and strengthen the scanning of short axis section of high large artery.

Congenital anomalies of the pulmonary arterial system in a paediatric cohort: a single- center 28-year experience

“…(19) Consistently with previous reports, angiography or CT con rmed our diagnosis. (17) (19) These imaging methods can also depict collateral vessels that may be present in these patients, as demonstrated in our cohort. Angiography was the diagnostic technique in two patients due to the fact that they were diagnosed 25 years ago when CT was not widely used in our centre.…”

“…(3)(17) As shown previously, UAPA was misdiagnosed by echocardiography in another patient. (19) A plausible explanations for this could be the misdiagnosis of the PDA as a PA branch or the insu cient awareness of this entity. (19) Consistently with previous reports, angiography or CT con rmed our diagnosis.…”

“…(19) A plausible explanations for this could be the misdiagnosis of the PDA as a PA branch or the insu cient awareness of this entity. (19) Consistently with previous reports, angiography or CT con rmed our diagnosis. (17) (19) These imaging methods can also depict collateral vessels that may be present in these patients, as demonstrated in our cohort.…”

Congenital unilateral absence of right pulmonary artery with VSD and wide aortopulmonary window in an adult patient: a case report

“…Unilateral absence of the pulmonary artery is twice as common on the right side 2 . Due to the lack of an adequate number of these cases, the prevalence of left-sided versus right-sided UAPA shows discrepancies that vary from study to study 2 , 5 . The involution of the proximal sixth aortic arch and the persistence of the connection of the intrapulmonary pulmonary artery to the distal sixth aortic arch causes the absence of the pulmonary artery 2 .…”

Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literature

“…1 It is important to note that patients who develop pulmonary hypertension tend to have poorer prognosis. 5 In the younger cohort, early revascularisation is an option, however this is contraindicated in older patients as the intrapulmonary arteries tend to be narrowed or obstructed by fibrosis, causing anastomosis to be impossible. 1 In severe cases of haemoptysis or pulmonary haemorrhage such as our second case, selective embolization, lobectomy or even pneumonectomy should be considered.…”