Unilateral pulmonary artery agenesis presenting with hemoptysis: Treatment by embolization of systemic collaterals

Reñé, Mercedes; Sans, Jordi; Domínguez, Juan M.; Sancho, C.; J, Valldeperas

doi:10.1007/bf00239422

Cited by 45 publications

(11 citation statements)

References 17 publications

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“…Although pneumonectomy with ligation of collaterals or reanastomosis of the peripheral pulmonary artery with the main pulmonary artery is a more definitive treatment, these major operations carry significant risks and may not be feasible in the emergent setting. Transcatheter embolization of aortopulmonary collaterals, either alone or as an adjunct to surgery, has shown to be a safe and effective treatment of hemoptysis related to PIPA in a small number of case reports ( 5 , 6 , 7 ).…”

Section: Discussionmentioning

confidence: 99%

Proximal interruption of the pulmonary artery: Transcatheter embolization for emergent management of massive hemoptysis

Liu

Monroe

Kogut

2013

Radiology Case Reports

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Transcatheter embolization is the first-line treatment for massive hemoptysis and recurrent intractable hemoptysis. Proximal interruption of the pulmonary artery is a rare congenital anomaly characterized by hypertrophy and neovasculsarity of bronchial and nonbronchial aortopulmonary collaterals; hemoptysis complicates a minority of cases. We present a case of unilateral proximal interruption of the left pulmonary artery associated with a right-sided aorta, presenting in adulthood with hemoptysis. The patient was managed emergently with bronchial, intercostal, and inferior phrenic artery embolization.

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Section: Discussionmentioning

confidence: 99%

Proximal interruption of the pulmonary artery: Transcatheter embolization for emergent management of massive hemoptysis

Liu

Monroe

Kogut

2013

Radiology Case Reports

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“…Patients who develop pulmonary hypertension can be treated medically with vasodilator therapy [ 11 , 12 ]. Hemoptysis may be self-limiting, selective embolization of the systemic collaterals and in selected cases pneumonectomy of the affected side may be required for massive hemoptysis [ 13 , 14 ].…”

Section: Discussionmentioning

confidence: 99%

Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS

Saladi

Roy

Diaz‐Fuentes

2018

Respiratory Medicine Case Reports

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Unilateral pulmonary artery agenesis (UPAA) is a rare malformation that can present as an isolated anomaly or may be associated with certain congenital cardiac anomalies, such as tetralogy of Fallot, atrial septal defect, coarctation of aorta, right aortic arch, truncus arteriosus and pulmonary atresia. Clinical presentation is non-specific which makes the diagnosis elusive; chronic dyspnea, hemoptysis or recurrent infections are the most common manifestations. Patients may remain asymptomatic until adulthood. There is no definitive treatment for patients with UPAA. Acute respiratory distress syndrome (ARDS) is usually a bilateral disease, unilateral ARDS has been described after lung resection or trauma. We present a case of a 39 year-old woman who developed unilateral ARDS and was later diagnosed with isolated UPAA.

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“…Treatment options of UPAA involve embolization of the abnormal systemic to pulmonary collateral vessels in cases presenting with hemoptysis, and even in few cases, pneumonectomy of the affected lung may even be essential. [ 1 10 ]…”

Section: Discussionmentioning

confidence: 99%

Unilateral acute respiratory distress syndrome with contralateral pulmonary artery agenesis: A rare scenario

Mishra¹,

Chaudhuri²,

Singh³

et al. 2018

Anesth Essays Res

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Unilateral pulmonary artery agenesis (UPAA) is a rare condition where the patient may remain asymptomatic for a long period till adulthood. Presentation may be in the form of dyspnea, cough, hemoptysis, decreased exercise tolerance, and recurrent respiratory tract infections. Ventilation–perfusion mismatch and excessive blood flow to the normal lung may eventually lead to unilateral acute respiratory distress syndrome (ARDS). We present a case of a 40-year-old gentleman with nonresolving pneumonia who was diagnosed to have unilateral ARDS due to UPAA. Even though ARDS involves bilateral lung, unilateral ARDS which does not show resolution with lung protective strategies should always raise the suspicion of a rare disease like UPAA among clinicians. To date, there is no specific prescribed treatment for UPAA.

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Unilateral pulmonary artery agenesis presenting with hemoptysis: Treatment by embolization of systemic collaterals

Cited by 45 publications

References 17 publications

Proximal interruption of the pulmonary artery: Transcatheter embolization for emergent management of massive hemoptysis

Proximal interruption of the pulmonary artery: Transcatheter embolization for emergent management of massive hemoptysis

Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS

Unilateral acute respiratory distress syndrome with contralateral pulmonary artery agenesis: A rare scenario

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