Unilateral Sensorineural Hearing Loss in Preschool Children

Isolated Cochlear Nerve Hypoplasia with Various Internal Auditory Meatus Deformities in Children

“…Unilateral profound sensorineural hearing loss in children has been a rather "common" disorder for otologists. The prevalence is around 0.1% to 0.2% worldwide, [1][2][3][4] and this disorder has been attributed to causes such as postnatal viral infection, sudden idiopathic deafness, sequelae of otitis media, prenatal or perinatal problems, and hereditary disorders, including anomalies. We recently reported a few cases of isolated cochlear nerve hypoplasia without inner ear anomalies, with and without narrowing of the internal auditory meatus (IAM), 5,6 and advocated this disorder as one of the causes of juvenile or adolescent unilateral profound deafness.…”