“…Mild ventriculomegaly is assumed when the width of the atria of lateral ventricle is from 10 to 12 mm, moderate from 12.1 to 14.9, while severe when equal or exceeding 15 mm, which is often associated with an unfavorable outcome [Romero et al, 1988; Gaglioti et al, 2005]. Congenital unilateral severe ventriculomegaly or hydrocephalus is rarely described, with only few reports in the literature [Husag et al, 1976; Wilberger et al, 1983; Oi et al, 1985; Dorwling‐Carter et al, 1987; Gaston and Jones, 1989; Nakamura et al, 1989; Anderson et al, 1993; Tsao et al, 1996; Chudley et al, 1997; Schulman et al, 2000; Durfee et al, 2001]. Congenital unilateral ventriculomegaly associated with sensorineural hearing loss was assigned by Chudley et al 1997 who delineated the new autosomal recessive disorder “Chudley–McCullough syndrome” and further similar cases were described (OMIM 604213).…”