Unraveling the Trio of Interrupted Descending Aorta, Aortic Stenosis, and Bicuspid Aortic Valve: A Complex Cardiovascular Conundrum

Abstract

Interrupted descending aorta (IDA) is an extremely rare congenital heart defect characterized by a complete loss of connection between the ascending and descending aorta. This condition is typically diagnosed in infancy or early childhood, but there have been very few cases reported in adulthood. Here, we present a unique case of an IDA in a 16-year-old patient with concomitant aortic stenosis (AS) and bicuspid aortic valve (BAV), making it an extremely rare scenario. This case highlights the importance of early diagnosis and appropriate management in patients with an IDA, particularly when in association with other cardiovascular abnormalities.

Marfanoid to Mortality: A Case Report on Sudden Cardiac Death Due to Aortic Dissection in a Young Male With Marfanoid Habitus

“…The compromised hemodynamics and the intricate vascular pathology in this case underscore the challenges faced by clinicians in stabilizing patients with such advanced cardiovascular complications [9]. The wide pulse pressure observed in the blood pressure readings further reflects the severity of the hemodynamic compromise and emphasizes the urgency for intervention [10]. The rapid clinical deterioration posed a considerable challenge, raising questions about the optimal timing and feasibility of operative intervention in such critical cases.…”