Unresectable Leiomyosarcoma Of The Inferior Vena Cava With Right Atrium Tumor Thrombus: When To Deem This Tumor Inoperable? A Case Report And Literature Review.

Abstract

Background Leiomyosarcomas (LMS) of the inferior vena cava (IVC) are a rare form of retroperitoneal malignancy and their venous extension to the right atrium is an even rarer event. These tumors pose a unique surgical challenge and often require a multidisciplinary team-based approach for their surgical treatment. Case presentation: We present a case of a 68-year-old male with primary LMS of the IVC with a tumor thrombus extending into the right atrium that was initially deemed inoperable. Conclusions After extensive neoadjuvant chemo-radiation with minimal tumor effect, the patient underwent en-bloc surgical resection of the tumor along with removal of the infrarenal IVC and right kidney and adrenal without the need for cardiopulmonary bypass.