Unusual aberrancy of right coronary artery (RCA) in patient with double-outlet right ventricle (DORV) with pulmonary stenosis (PS)

Abstract

The incidence of coronary artery anomalies in double-outlet right ventricle (DORV) or tetralogy of Fallot (TOF) has been reported to be 2% to 10%. Surgical correction in such a scenario, across a narrowed and underdeveloped right ventricular outflow tract (RVOT), poses a significant challenge and has been associated with increased morbidity and mortality. These combinations at times may change the approach of primary repair to one of initial palliation. Single coronary artery, meaning anomalous origin of the right coronary artery from the left anterior descending artery, is a benign and very rare coronary artery anomaly. Here, we report the case of an 11 year-old boy with double-outlet right ventricle (DORV) with pulmonary stenosis (PS) where pre-operative catheterisation and multi detector CT angiography (MDCT) revealed anomalous right coronary artery arising from left anterior descending artery.