Unusual Case of an 18-Year-Old Heart Transplant Recipient With Endocardial Fibroelastosis

Fuchs, U; Zittermann, Armin; Schulz, Uwe; Tenderich, Gero; Raute-Kreinsen, U; Minami, Kazutomo; Körfer, Reiner

doi:10.1016/j.transproceed.2006.02.097

Cited by 3 publications

(1 citation statement)

References 6 publications

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“…There was a Korean paper about idiopathic restrictive cardiomyopathy in children, but the pathologic diagnosis was not investigated 8). Several cases with EFE in young adults have also been reported in other countries 4)9). Interestingly, however, our patient showed an unusually benign course despite extensive fibroelastosis and remained in good functional status until her 50s.…”

Section: Discussionmentioning

confidence: 73%

Endocardial Fibroelastosis in a 57-Year-Old Transplant Recipient

et al. 2010

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Endocardial fibroelastosis (EFE) is characterized by deposition of collagen and elastin leading to ventricular hypertrophy and diffuse endocardial thickening. Here we report (for the first time in Korea) the case of a EFE presenting with heart failure. The patient was a 57-year-old woman who had complained of dyspnea on exertion {New York Heart Association (NYHA) functional class 3} and abdominal distension at the time of hospital admission. Echocardiography showed severe diastolic dysfunction with normal systolic function. On MRI, the contrast-enhanced delayed myocardial image demonstrated hyperenhancement in the endocardium. Owing to progressive heart failure, the patient was transplanted. Histological examination of the explanted heart showed irregularly thickened endocardium with fibrosis and elastosis in the both ventricles, compatible with the diagnosis of EFE.

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Section: Discussionmentioning

confidence: 73%