Unusual Presentation of Primary Pleomorphic Rhabdomyosarcoma of Heart: Complete Atrioventricular Block and Severe Mitral Regurgitation

Abstract

Primary cardiac tumours are rare and difcult to diagnose because most are asymptomatic or have varied non-specic presentations. This report describes a 29-year-old man presenting with complete heart block, primary cardiac tumour in the left atrium, and severe mitral regurgitation. In view of the primary severe mitral regurgitation and complete heart block, mitral valve repair and pacemaker insertion were planned. Mitral valve repair was done with 29mm St Jude tailor annuloplasty ring, and the biopsy was taken from the nodules noted in the left atrium; temporary right ventricular epicardial pacemaker implantation and CABG with SVG to PDA graft were done to look for the recovery of complete heart block. Histopathological examination revealed pleomorphic rhabdomyosarcoma. The patient developed renal failure and liver failure during the postoperative period and expired after 10 days