Abstracts Urethral leiomyoma is a rare benign tumor arising from smooth muscles of urethra. These tumors are more common in women than men, and few cases were reported in the literature. Presentation with acute urinary retention was rare. Proximal segment of urethra was commonly affected than the distal segment. We report here a case of urethral leiomyoma at the distal urethra presenting with acute urinary retention.