Use of FACIAL ARTERY MUSCULOMUCOSAL and Turbinate Flaps for Rapp Hodgkin Syndrome

Abstract

Rapp Hodgkin Syndrome (RHS), is a subtype of Ectodermal Dysplasias (EDs), which has various manifestation. Here, we report a case on repair of the palatal cleft in an 18 year old girl, having RHS, with combination of facial artery musculomucosal (FAMM) flap and inferior turbinate flaps (ITF), at

Facial Reconstruction Using Facial Artery Myomucosal Flap: A Comprehensive Review

“…However, if excessive tension raises concerns over potential contracture, the donor site can choose to be skin grafted, left to granulate, or closed with buccal fat pad advancement [ 2 ]. Saboury et al discussed a rare case of Rapp-Hodgkin syndrome; the authors further recommended the use of a combination of FAMM and inferior turbinate flaps for the treatment of the wide cleft [ 51 ]. As mentioned by Pribaz et al, the FAMM flap, which is a nearby flap, is suitable for reconstructing the lip and vermilion.…”

“…There are several minor complications that are commonly associated with the use of the FAMM flap in the literature. These include partial or complete flap necrosis, dehiscence, venous congestion, hematoma, and infections [ 2 , 51 ]. There are two factors that are highly related to an increased risk of having partial flap necrosis: previous neck dissection and previous radiation therapy [ 1 ].…”