Use of high-dose intravenous corticosteroid treatment in a child with scleredema

Kurtoğlu, Selim; Yüksel, Şaban; Gündüz, Zübeyde; Per, Hüseyin; Narın, Nazmi; Kontaş, Olgun; Özdemır, Mehmet Akif; Çaksen, Hüseyîn

doi:10.1016/j.jemermed.2003.12.006

Cited by 7 publications

(3 citation statements)

References 11 publications

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“…Scleredema that arises after an infection presents a more abrupt onset. Typically, scleredema symptoms start a few weeks after the initial infection [ 7 , 8 ]. The cervicofacial region is primarily affected.…”

Section: Discussionmentioning

confidence: 99%

Scleredema Adultorum of Buschke Associated With Diffuse Eosinophilia and Hepatitis B Virus Infection

Patel¹,

Vora²,

Chaudhary³

et al. 2023

Cureus

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Scleredema adultorum of Buschke is a rare condition that presents as a scleroderma mimic and portends a diagnostic challenge to the clinician. It may be associated with monoclonal gammopathy, upper respiratory tract infection, or type II diabetes mellitus. In addition, it is associated with dermal collagen and aminoglycan deposits that cause the skin to thicken and stiffen. Typically, thickening and tightening begin in the neck and progress to the upper body, including the face, scalp, shoulders, and trunk, but sparing the palms and soles. Patients with minor skin involvement may not suffer any symptoms, whereas those with significant skin disease may develop stiffness and functional impairment. There are rare reports linking scleredema adultorum of Buschke with several infections such as human immunodeficiency virus infection, acquired immunodeficiency syndrome-related lipodystrophy syndrome, and streptococcal infection of the upper respiratory tract. Here, we present a case of scleredema adultorum of Buschke associated with hepatitis B infection.

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Section: Discussionmentioning

confidence: 99%

Scleredema Adultorum of Buschke Associated With Diffuse Eosinophilia and Hepatitis B Virus Infection

Patel¹,

Vora²,

Chaudhary³

et al. 2023

Cureus

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“…11 Various immunosuppressants, such as glucocorticoids, cyclosporine and methotrexate, have also been used with limited success. 12 Prognosis of patients with scleroedema is dependent on the class to which it belongs. Mortality in scleroedema is rare and has occurred owing to respiratory or cardiac involvement.…”

Section: Discussionmentioning

confidence: 99%

Scleroedema of Buschke in Conjunction with Ovarian Carcinoma: Rare Association of a Rare Disease

Dev

Kumar

Sharma

et al. 2020

Journal of the Royal College of Physicians of Edinburgh

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Scleroedema is a rare clinical condition characterised by diffuse woody induration of skin commonly associated with diabetes mellitus, infections and monoclonal gammopathy. Its association with ovarian malignancy has not been reported. We report a case of a 56-year-old female with rapidly progressing skin thickening of limbs, face and trunk for 1 year and abdominal distension for 3 months. Patient had thickened skin, mask-like facies and ascites on examination. Atypical cells were seen in ascitic fluid. Contrast-enhanced computerised axial tomography scan of abdomen was suggestive of ovarian malignancy. Markers for autoimmune disorders were negative. CA 125 was elevated. Other causes of sclerodermiform-like syndrome were ruled out. Histopathology of skin biopsy was definitive of scleroedema. Diagnosis of scleroedema associated with ovarian malignancy was made based on temporal association, exclusion of other causes and histopathological findings. To our knowledge this is the first reported case of scleroedema associated with ovarian tumour.

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“…Tumor necrosis factor alpha (TNF-alpha) blocking agent-, infliximab, induced scleredema has been reported. Infection-related scleredema is characterized by a sudden onset and often shows complete clinical recovery after several months (1,7,8). Monoclonal gammopathy-associated scleredema is characterized by slow onset and slow progression; usually spontaneous recovery does not occur (2,9).…”

Section: Introductionmentioning

confidence: 99%

Scleredema Diabeticorum in a Patient with Type 2 Diabetes Mellitus

Sarı¹,

Durmaz²,

Bozdoğan³

et al. 2016

tjem

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Use of high-dose intravenous corticosteroid treatment in a child with scleredema

Cited by 7 publications

References 11 publications

Scleredema Adultorum of Buschke Associated With Diffuse Eosinophilia and Hepatitis B Virus Infection

Scleredema Adultorum of Buschke Associated With Diffuse Eosinophilia and Hepatitis B Virus Infection

Scleroedema of Buschke in Conjunction with Ovarian Carcinoma: Rare Association of a Rare Disease

Scleredema Diabeticorum in a Patient with Type 2 Diabetes Mellitus

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