“…2 In the female genital tract, uterine corpus is the most common site for AMLs followed by cervix, vagina, ovary, fallopian tube, broad ligament and parametria. 2,3 As per definition of World Health Organization (WHO), perivascular epithelioid cell tumors (PEComas) is a family of neoplasms, which includes renal or extrarenal AML, lymphangioleiomyomatosis and clear cell tumors of diverse sites. 3,5 AML may be categorized as sporadic and syndromic (accompanying TS) types.…”