Uterus Didelphia with Left Hematocolpos and Ipsilateral Renal Agenesis

Abstract

We report a rare case of uterus didelphia with left hematocolpos and ipsilateral renal agenesis, associated with contralateral vesicoureteral reflux and chronic atrophic pyelonephritis. In the literature 9 cases of uterus didelphia with left hematocolpos but without concomitant reflux and recurrent bacterial pyelonephritis are reported. The embryogenesis of müllerian duct abnormalities, associated clinical findings, including abdominal tenderness and pelvic mass, diagnostic modalities of cystoscopy, excretory urography, laparoscopy and hysterosalpinography are discussed. Early accurate diagnosis and treatment will decrease morbidity and unnecessary surgical procedures.

Asymmetric lateral distribution of obstructed hemivagina and renal agenesis in women with uterus didelphys: institutional case series and a systematic literature review

“…Consequently, we decided to exclude the 12 papers published in the period 1980 to 1985 described in the Morgan et al review (5,6,(30)(31)(32)(33)(34)(35)(36)(37)(38)(39). However, we retrieved four other articles published in the same time span but not cited by Morgan et al (40)(41)(42)(43).…”

Uterus didelphys with obstructed hemivagina and renal agenesis : mri findings

“…The cascade of events in the development of the female genital tract occurs during the 6 th and 22 nd week of gesta- embryologic relationship between the mesonephric (Wolffian) ducts and the paramesonephric ducts. Various teratologic influences are believed to cause concomitant urologic and gynaecologic malformations (4)(5)(6) MRI, with its superior soft tissue resolution, often leads to a straightforward diagnosis of complex Müllerian duct abnormalities. Therefore it is considered the best noninvasive tool in the work-up of malformations of the urogenital tract.…”

Urological Complications Associated to Uterus Didelphys with Unilateral Hematocolpos A Case Report and Review of the Literature

“…The isolated incidence of unilateral renal agenesis varies from 1/500 to 1/1,300 being associated with genital anomalies in 25-70% [3][4][5]. The incidence of uterus didelphys is between 1 per 2,000 and 1 per 28,000 with 43% ipsilateral renal agenesis [6,7], In women with a solitary kidney, 55-70% of associated genital anomalies are also reported [3].…”

“…The incidence of uterus didelphys is between 1 per 2,000 and 1 per 28,000 with 43% ipsilateral renal agenesis [6,7], In women with a solitary kidney, 55-70% of associated genital anomalies are also reported [3]. In a study of 52 women with unilateral renal agen esis, Thompson and Lynn [8] found 32 % of associated uterus didel phys.…”

“…The proportion of associated urological complications is note worthy in 10% of cases: difficult micturition [21,23], urinary fre quency [3,24], urinary tract infection [9,25], pain radiating to ure thra [5], stress urinary incontinence [26], and 5 particularly remark able cases of acute urinary retention, 4 as a first symptom [13,[27][28][29] and the other preceded by dysuria [17], In our own cases, the urological symptomatology was the main cause of consultation. Therefore, an acute urinary retention in a teenager must alert the urologist in order to consider this entity among the diagnostic pos sibilities.…”