Since the introduction of the related variety concept in 2007, a number of studies have been undertaken to analyse its effect on economic development. Our review of 21 studies makes clear that most studies find support for the initial hypothesis that related variety supports employment growth, though some studies suggest that the growth effects of related variety may be specific to knowledge-intensive sectors only. From the review, we list a number of further research questions regarding methodology, the role of unrelated variety, different forms of relatedness and the effect of related variety on knowledge production and entrepreneurship.ARTICLE HISTORY