Vascular Anomalies Classification: Recommendations From the International Society for the Study of Vascular Anomalies

Abstract

Background Skin disorders in neonates can be regarded as determining concepts for prognosis and genetic counseling. Few studies have so far been conducted on determining and recording the relative frequency of skin disorders. The present study was therefore conducted to investigate skin manifestations and their relationship with other variables in the neonates hospitalized in the neonatal intensive care unit (NICU). Methods The present cross-sectional study was conducted on 403 neonates, hospitalized in the NICU of Rasoul Akram Hospital in 2014 and selected using convenience sampling. The data collected from

Choice of Treatment Options for Cystic Lymphstic Malformations in the Head and Neck Region: Treatment Experience of 81 Children

“…The size of LMs up to 100 cm 2 was evaluated as small, 100-199 cm 2 -middle, 200-299 cm 2 -large and more than 300 cm 2 -gigantic. The result of the treatment of LM was determined by the percentage of reduction in the lesion size [3,10] as excellent (decrease by more than 90%), good (50-89%), satisfactory (20-49%) and unsatisfactory (less than 20% reduction in size).…”

“…In 1982, a landmark article by Mulliken and Glowacki suggested a classification system designating vascular ano malies as either tumours or malformations accor ding to their biologic and pathologic features [2]. This system was adopted by the international society for the study of vascular anomalies (ISSVA) and was last updated in 2014 [3]. Vascular malformations are classified as capillary, venous, lymphatic, arterial, and mixed lesions, depending on their vascular tissue of origin.…”

Making Sense of “Red Birth Marks”

“…What a useful tool the vascular anomalies classification described by Wassef et al 1 would have been during my medical training! As a pediatric resident in the 1980s, I was frequently perplexed by the many red "birth marks" I was confronted with while performing newborn and well-child examinations.…”

“…But rules (as well as classifications) were made to be broken (or amended), and Wassef et al 1 have done just that with the latest ISSVA classification, summarized in this month's journal. As our knowledge of the presentation, life cycle, histopathology, and radiologic characteristics of vascular lesions has grown, it has become clear that there are "exceptions and additions" to the 1996 classification.…”

Primary Intestinal Lymphangiectasia and its Association With Generalized Lymphatic Anomaly

“…Although currently unused, congenital lymphatic anomalies have historically been classified according to their anatomopathological characteristics (3)(4)(5); however, these classifications sometimes overlap and are generally quite confusing. To obtain a homogeneous classification and to promote its use, the international society for the study of vascular anomalies (ISSVA) published a classification scheme in 1996, which was expanded and updated in 2014 (6).…”