Vascularite gangréneuse juvénile du scrotum au cours de la maladie de Behçet

Juvenile gangrenous vasculitis of the scrotum: systematic review

“…Lesions measured between 0.5 cm and 3 cm in diameter. Disease onset was acute and painful in 76.47% of patients ( n = 13) 3,5,7–12 . Physical examination did not reveal a palpable connection to the testicle, lymphadenopathy, urinary symptoms, mucous membrane involvement, or other cutaneous lesions in the majority of cases 5,8,11–16 .…”

“…An association between JGVS and Behcet's Disease (BD) was noted in one patient (5.8%) 9 . The patient had an exacerbation of BD that manifested as multiple mouth ulcers, necrotic pseudofollicles in the back and thighs, inflammatory talalgia, and arthritis of the right ankle.…”

“…A great variety of empiric antibiotics was given to patients. Progressively tapering dosage of corticosteroids (intramuscular injection of betamethasone 4 mg daily for 2–4 weeks or oral prednisolone [0.5 mg/kg/day] for 3–4 weeks) was prescribed for six patients (37.5%) 5,7–9,14,18 …”

“…The patient had an exacerbation of BD that manifested as multiple mouth ulcers, necrotic pseudofollicles in the back and thighs, inflammatory talalgia, and arthritis of the right ankle. He was febrile and had multiple painful scrotal ulcers 9 . A total of 64.7% ( n = 11) of patients had concomitant or a recent history of upper respiratory tract symptoms 3,5,7,8,10–13,15,16,18 .…”

“…Disease onset was acute and painful in 76.47% of patients (n = 13). 3,5,[7][8][9][10][11][12] Physical examination did not reveal a palpable connection to the testicle, lymphadenopathy, urinary symptoms, mucous membrane involvement, or other cutaneous lesions in the majority of cases. 5,8,[11][12][13][14][15][16] One patient had local edema and erythema with inguinal lymphadenopathy.…”