Wandering spleen with horseshoe kidney a rare occurrence

Abstract

HighlightsWandering spleen with horseshoe kidney is a rare occurrence with less than 3 cases reported worldwide.Delay in diagnosis would result is increased mortality.Splenopexy is preferred in children with the exception of grossly infarcted spleen.Splenectomy is the treatment of choice in torsion of spleen with infarct.

‘Wandering spleen with acute torsion’ : a rare indication for splenectomy in an adult, complicated by postoperative splanchnic venous thrombosis and intestinal gangrene

“…WS is reported to be associated with a variety of conditions such as hypermobile colon, Prune belly syndrome, horseshoe kidney, gastric volvulus, intestinal malrotation, renal agenesis, diaphragmatic eventration and congenital diaphragmatic hernia 4 5 11 12. A rare familial association of WS in two sisters has been reported by Ben Ely et al 13.…”

“…The absence of laxity in splenic ligaments will lead to a hypermobile spleen, which may be ectopic in position and attached only by an elongated vascular pedicle 9 10. Congenital absence or laxity of the ligaments is due to the failure of the dorsal mesogastrium to fuse with the posterior abdominal wall during the second month of embryogenesis 3 4 11. Laxity of ligaments can also be acquired secondary to trauma, and splenomegaly due to malaria and haematological disorders such as hereditary spherocytosis, thalassaemia and lymphomas or due to the hormonal effects of pregnancy 4 5 9.…”