Woolly hair naevi with systematized linear epidermal naevus

Wright, S.; Lemoine, Nick R.; Leigh, Irene M.

doi:10.1111/j.1365-2230.1986.tb00444.x

Cited by 25 publications

(10 citation statements)

References 3 publications

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“…Half of the cases reported have been associated with an epidermal or a congenital nevus, usually located ipsilaterally on the neck or arms. 246,249,250 WHN syndrome has been reported with epidermal nevi, boney abnormalities, precocious puberty, speech and dental anomalies. 251,252 WHN can follow Blaschko lines, suggesting that it may be a mosaic disorder.…”

Section: Trichorrhexis Invaginatamentioning

confidence: 98%

The genetics of hair shaft disorders

Cheng

Bayliss

2008

Journal of the American Academy of Dermatology

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Section: Trichorrhexis Invaginatamentioning

confidence: 98%

The genetics of hair shaft disorders

Cheng

Bayliss

2008

Journal of the American Academy of Dermatology

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“…Wise first described the woolly hair nevus in 1927. 3,11 However, others have reported no change 12 in diameter and even an increased 13 diameter. 4,5 Less frequent associations of woolly hair nevus include ocular defects, 6 precocious puberty, 7 digital abnormalities, auditory defects, 8 and dental abnormalities.…”

Section: Discussionmentioning

confidence: 97%

Hair Follicle Miniaturization in a Woolly Hair Nevus

Veraitch

Perez

Hoque

et al. 2016

The American Journal of Dermatopathology

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Woolly hair nevus is a mosaic disorder characterized by unruly, tightly curled hair in a circumscribed area of the scalp. This condition may be associated with epidermal nevi. We describe an 11-year-old boy who initially presented with multiple patches of woolly hair and with epidermal nevi on his left cheek and back. He had no nail, teeth, eye, or cardiac abnormalities. Analysis of plucked hairs from patches of woolly hair showed twisting of the hair shaft and an abnormal hair cuticle. Histopathology of a woolly hair patch showed diffuse hair follicle miniaturization with increased vellus hairs.

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“…Over the flexures, these lesions may become macerated and foul smelling. Non-epidermolytic verrucous epidermal naevi have been associated with scalp (wooly hair naevi) [3]. Malignant degeneration has been reported to occur rarely within these lesions mostly over 40 y of age.…”

Section: Discussionmentioning

confidence: 99%

Systematised Epidermal Nevus - A Case Report

Dhanaraj

Ramalingam

2015

JCDR

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A 20-year-old female born to nonconsanguineous parents was seen in our outpatient department with complaints of raised skin lesions all over the body since birth. There was a history of darkening and thickening of the lesions with age. The growth and developmental history were normal and there was no history of seizures or learning difficulty, altered vision or difficulty in hearing.On examination there were multiple pigmented macules and hyperkeratotic papules arranged in streaks and whorls over the forehead, left side of face extending from the left lower eyelid upto mid face, as a linear streak from near the angle of mouth left side to the neck, as a linear streak over the temple and adjoining the upper eyelid and side of face on the right side. Similar lesions were seen as streaks on both sides of the neck [Table/ Fig-1], as linear streaks extending from posterior aspect of neck to the upper back [Table/ Fig-2], as whorls over sides of chest and abdomen and as linear streaks over both lower limbs. The oral and genital mucosa were found to be normal. Histopathology of the lesion taken from left leg revealed hyperkeratosis with moderate acanthosis [Table/ Fig-3]. There was uniform pigmentation over the basal zone. In the dermis there were prominent hair follicles and sebaceous glands. The examination of other systems did not reveal any abnormality. There were no skeletal deformities. Examination of the nervous system was also observed to be normal. Magnetic resonance imaging (MRI) brain did not reveal any abnormality. IQ testing was done and the patient was found to be of normal intelligence.

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Woolly hair naevi with systematized linear epidermal naevus

Cited by 25 publications

References 3 publications

The genetics of hair shaft disorders

The genetics of hair shaft disorders

Hair Follicle Miniaturization in a Woolly Hair Nevus

Systematised Epidermal Nevus - A Case Report

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