“…There have been several associations between woolly hair nevus and ophthalmologic (heterochromia iridis, persistent papillary membrane), [16,17], auditory (auditory disturbance), [18], renal, cutaneous (pigmentary demarcation lines, linear epidermal nevus, white sponge nevus), [2,13,16,19], dental (diastema, decayed lower canine teeth), [5,13], and skeletal (growth impairment, brachyphalangy), [18] manifestations. In half the cases, patients with WHN have an ipsilateral verrucous epidermal nevus.…”