Wrist problems in patients with Ehlers-Danlos syndrome

Woerdeman, Leonie A. E.; Ritt, Marco J.P.F.; Meijer, Boaz; Maas, Mario

doi:10.1007/s002380050252

Cited by 6 publications

(4 citation statements)

References 8 publications

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“…Some patients with these diseases, have reported congenital joint and soft tissue contractures accompanying joint hypermobility, which is contrary to the hypothesis of this study. [46,47] In BJHS, a nonpathogenic polymorphism occurs due to minor variations in the extracellular matrix genes, for example collagen, elastin, and fibrillin. With MS, EDS and OI, major variations and variations in the protein-binding points occur in the extracellular matrix genes, leading to severe organ disorders.…”

Section: Discussionmentioning

confidence: 99%

“…With MS, EDS and OI, major variations and variations in the protein-binding points occur in the extracellular matrix genes, leading to severe organ disorders. [47,48] In the literature, favorable effects associated with GJH and BJHS have also been reported. Hypermobility has been demonstrated to provide a protective effect against bone injury by enhancing the stretching property of the ligament and joint capsule in cases of spinal cord injuries in childhood.…”

Section: Discussionmentioning

confidence: 99%

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The Relationship Between Generalized Joint Hypermobility and Adhesive Capsulitis of the Shoulder

et al. 2013

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Amaç: Bu çalışmada generalize eklem hipermobilitesi (GEH) ve omzun adeziv kapsüliti (AK) arasındaki muhtemel ilişki araştırıldı. Hastalar ve yöntemler:Çalışma grubunda 120'si AK tanılı ve kontrol grubunda 120'si primer subakromiyal sıkışma sendromu tanılı olmak üzere, toplam 240 hasta çalışmaya dahil edildi. Her iki grupta da ağrı şiddeti, omuz eklem hareket açıklığı, fonksiyonel değerlendirme, engellilik ve hipermobilite değerlendirildi. Generalize eklem hipermobilitesi Beighton skoru, benign eklem hipermobilite sendromu (BEHS) ise revize Brighton kriterleri ile değerlendirildi. Bulgular: Adeziv kapsülit grubunda, GEH sadece bir hastada (%0.08) olmak üzere oldukça nadir (p<0.05) saptanırken, BEHS'ye rastlanmadı. Kontrol grubunda ise dokuz hastada (%7.5) GEH, beş hastada (%4.2) BEHS gözlendi.Sonuç: Çalışma bulgularımız, GEH'in AK gelişimi için koruyucu veya önleyici bir faktör olabileceğini göstermektedir. Klinik pratikte, GEH olan hastalarda gelişen omuz ağrılarında, tablonun AK'ye dönüşümü açısından daha iyimser olunabileceğine inanıyoruz. Generalize eklem hipermobilitesi bulunan hastalarda AK gelişimi söz konusu ise, bu hastalar tedaviye daha iyi yanıt verebilir.Anahtar sözcükler: Adeziv kapsülit; benign eklem hipermobilite sendromu; sıkışma sendromu.Objectives: This study aims to investigate the possible relationship between generalized joint hypermobility (GJH) and adhesive capsulitis (AC) of the shoulder. Patients and methods:A total of 240 patients were enrolled in this study, including 120 patients diagnosed with AC in a study group and 120 patients diagnosed with primary subacromial impingement syndrome in the control group. We evaluated the pain severity, range of motion of the shoulder joint, functional status, disability, and hypermobility in both groups. The Beighton score was used to evaluate the GJH while the revised Brighton criteria were utilized for the patients with benign joint hypermobility syndrome (BJHS). Results:In the adhesive capsulitis group, GJH was significantly rare (p<0.05) with only one patient (0.08%) whereas BJHS was not found. In the control group, nine patients (7.5%) had GJH, and five (4.2%) had BJHS. Conclusion:Our study results suggest that GJH may be a protective or preventive factor in the development of AC. In clinical practice, we believe that in GJH patients we can be more optimistic regarding the concern of the conversion of shoulder pain to AC. If this has already taken place, then these patients may respond more positively to treatment in cases involving GJH.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

The Relationship Between Generalized Joint Hypermobility and Adhesive Capsulitis of the Shoulder

et al. 2013

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“…3,4,20 Up to 70% of Ehlers-Danlos syndrome patients, mostly with the hypermobility type, reportedly have painful midcarpal laxity. 21 This generally tightens up with time. Therefore, in these patients the instability can be self-limiting.…”

Section: Pathophysiologymentioning

confidence: 91%

“…Therefore, in these patients the instability can be self-limiting. 5,21 Fig . 1 Ligaments involved in the development of palmar mid carpal instability.…”

Section: Pathophysiologymentioning

confidence: 99%

Demystifying Palmar Midcarpal Instability

2020

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Palmar midcarpal instability is an uncommon condition diagnosed clinically with a painful pathognomonic clunk on terminal ulnar deviation of the wrist. Various causes have been described, but congenital laxity of the carpal ligaments is thought to be a key contributor. Treatment commences with conservative measures. This includes proprioceptive training based on more recent concepts on the sensorimotor function of the wrist. When these measures plateau, surgery is considered. The lack of high-level evidence and consensus on its cause continue to hamper our understanding and knowledge of this condition. The purpose of this review is to examine the current evidence to conceptualize this mysterious, yet infrequent phenomenon, and to provide an algorithm on its management.

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Midcarpal Instability

Higgin

Hargreaves

2017

Hand Clinics

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Wrist problems in patients with Ehlers-Danlos syndrome

Cited by 6 publications

References 8 publications

The Relationship Between Generalized Joint Hypermobility and Adhesive Capsulitis of the Shoulder

The Relationship Between Generalized Joint Hypermobility and Adhesive Capsulitis of the Shoulder

Demystifying Palmar Midcarpal Instability

Midcarpal Instability

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