Y-type congenital urethral duplication with normal dorsal urethra and small ventral fistula to perineal skin – 28th reported case

Meier, Donald E.; Latiff, Alfonso

doi:10.1016/j.epsc.2016.03.008

Cited by 6 publications

(10 citation statements)

References 13 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Several names have been used to refer to this pathology: congenital Y-type urethroperineal fistula, Y-type urethral duplication in a male, or Y-type congenital urethral duplication [4,5,7]. A few authors consider CUPF to be a congenital urethral duplication associated with a normal dorsal urethra and a small ventral fistula extending to the perineal skin [7], which could be categorized as a unique form or variation of urethral duplication [1,5,8]. The Effmann's classification describes different types of urethral duplication [7].…”

Section: Pediatr Urol Case Repmentioning

confidence: 99%

“…A few authors consider CUPF to be a congenital urethral duplication associated with a normal dorsal urethra and a small ventral fistula extending to the perineal skin [7], which could be categorized as a unique form or variation of urethral duplication [1,5,8]. The Effmann's classification describes different types of urethral duplication [7]. Per this classification, the type II A2 variety refers to complete urethral duplication in which a patient presents with 2 urethral meatuses.…”

Section: Pediatr Urol Case Repmentioning

confidence: 99%

“…Although both pathological entities show similar features on imaging studies [9,11], each condition requires different treatment [9]. In patients with urethral duplication, the functional ventral urethra needs to be transposed into a more eutopic position [3,7]. Despite such differences between these two conditions, several authors propose that CUPF should be classified as a true urethral duplication and not a urethral fistula [3,4,8,13].…”

Section: Pediatr Urol Case Repmentioning

confidence: 99%

“…Pressure atrophy from the heel of the fetal foot and a vascular accident have been viewed as possible etiologies of the anomalies [5,14]. The urethral opening of the fistula is located within the prostatic urethra, usually near the verumontanum or close to the bladder neck [1,[3][4][5][6][7][8][9][10][11][12][13][14]. Localization of the perineal opening of the fistula may often be observed between the base of the scrotum and the anus [1,3,4,8,9,11,12,13].…”

Section: Pediatr Urol Case Repmentioning

confidence: 99%

“…A segment of the fistula tract can get enlarged to form a saccular dilatation or a palpable cystic mass, particularly at its distal end [4,13,15]. According materials used to perform catheterization of the fistula the diameter of the fistula tract varies between the dimensions of a lachrymal probe (0.4 mm) and a 4F ureteral catheter (1.33 mm) [3,7,9]. The age of presentation varies between 9 days and 82 years [1,6].…”

Section: Pediatr Urol Case Repmentioning

confidence: 99%

See 4 more Smart Citations

Congenital urethroperineal fistula with scrotal localization: A case report

Ada¹,

Moustapha²,

Habou³

et al. 2018

j-pucr

View full text Add to dashboard Cite

A B S T R A C TA congenital urethroperineal fistula (CUPF) is a rare malformation that can be considered an unusual form of urethral duplication. A 3-year-old boy presented with an orifice in the middle of his scrotum through which urinary leakage was observed during micturition. Retrograde and voiding urethrocystograms showed a fistula tract extending from the prostatic urethra to his perineum. He was successfully treated with resection of the fistula performed via a perineal approach. No clinical sign and radiological evidence of disease were observed during his 4-month postoperative follow-up. Accurately distinguishing CUPF from a similar form of urethral duplication (type II A2-Y urethral duplication) is important for definitive treatment.

show abstract

Section: Pediatr Urol Case Repmentioning

confidence: 99%

Section: Pediatr Urol Case Repmentioning

confidence: 99%

Section: Pediatr Urol Case Repmentioning

confidence: 99%

Section: Pediatr Urol Case Repmentioning

confidence: 99%

Section: Pediatr Urol Case Repmentioning

confidence: 99%

See 3 more Smart Citations

Congenital urethroperineal fistula with scrotal localization: A case report

Ada¹,

Moustapha²,

Habou³

et al. 2018

j-pucr

View full text Add to dashboard Cite

show abstract

Urethropubic, Urethrocutaneous and Urethroperineal Fistulas

Doumanian

2022

Urinary Fistula

View full text Add to dashboard Cite

Retrograde urethrography in children: a decade of experience at a children’s hospital

et al. 2023

View full text Add to dashboard Cite

Background Retrograde urethrography (RUG) is a radiologic procedure that optimizes imaging evaluation of the urethra, particularly in settings of difficulty with micturition or urethral injury. Objective To review our experience with RUG at a large pediatric radiology practice. Materials and methodsWe conducted a retrospective review of medical records and fluoroscopic images of RUGs performed from January 2010 to December 2020. ResultsWe identified 180 RUG exams (median frequency 17 exams per year), all in male children (median age 13 years). The most common indications were stricture (42%; n=76), postsurgical evaluation (34%; n=62) and trauma (16%; n=29). The most commonly used catheter was Foley (40%; n=72), with a median catheter size of 5 French (Fr) for infants younger than 1 year, 7 Fr for children ages 1-5 years and 8 Fr for children older than 5 years. About a third of the children (57; 32%) had combined voiding cystourethrography (VCUG)-RUG exams. Water-soluble contrast agent, either 17% or 43% Cysto-Conray, was used. Most RUG exams were normal (46%; n=83). The most common urethral pathology was stricture (30%; n=54), commonly involving a bulbar urethra (n=26). Urethral trauma was seen in 11 children (6%), 10 bulbar and 1 membranous. Most children with stricture were surgically treated (n=40; 74%), whereas most children with trauma were conservatively treated (n=8; 73%). The remaining diagnoses included diverticula, polyps, valves, fistulas and duplications, constituting <17% of our sample; most of these were surgically treated. Four exams (2%) were non-diagnostic. RUG showed 89% sensitivity and 97% specificity compared to cystourethroscopy/VCUG findings. Technical difficulties occurred in 14 (8%) children (e.g., pain or inappropriate catheter seal). Conclusion Our experience indicates that when catheterization techniques are properly tailored, RUG provides a useful and successful radiologic method of evaluating the pediatric male urethra.

show abstract

Y-type congenital urethral duplication with normal dorsal urethra and small ventral fistula to perineal skin – 28th reported case

Cited by 6 publications

References 13 publications

Congenital urethroperineal fistula with scrotal localization: A case report

Congenital urethroperineal fistula with scrotal localization: A case report

Urethropubic, Urethrocutaneous and Urethroperineal Fistulas

Retrograde urethrography in children: a decade of experience at a children’s hospital

Contact Info

Product

Resources

About