Two cases of neurofibromatosis and intracranial arterial occlusive disease are reported. The radiographic and clinical features of these and twelve previously reported cases are reivewed.

Carotid arteriograms on three patients with unilateral pulsatile tinnitus demonstrated an ipsilateral atypical trigeminal artery extending from the cavernous portion of the internal carotid artery to form the posterior inferior cerebellar artery. Illustrations and a dissection of a human fetus with a similar finding show this artery crossing the cochlear nerve near its insertion in the pons. Evidence is presented suggesting that neurovascular compression of the eighth nerve is the source of pulsatile tinnitus in these patients.

Multiple cases of vascular abnormalities associated with the persistent trigeminal artery or a variant thereof are presented. A persistent otic artery variant is the only known such case in the literature.

No abstract